OOIR: Observatory of International Research

Papers

(The TQCC of Pediatric Rheumatology is 6. The table below lists those papers that are above that threshold based on CrossRef citation counts [max. 250 papers]. The publications cover those that have been published in the past four years, i.e., from 2021-01-01 to 2025-01-01.)

Article	Citations
Efficacy and safety of canakinumab in systemic juvenile idiopathic arthritis, the first Chinese experience	124
Bone mineral density and explanatory factors in children and adults with juvenile dermatomyositis at long term follow-up; a cross sectional study	80
CAR T cell therapy for refractory pediatric systemic lupus erythematosus: a new era of hope?	43
ANCA-negative eosinophilic granulomatosis with polyangiitis in a girl misdiagnosed as asthma and pulmonary tuberculosis	38
A narrative review of the literature on illness uncertainty in hypermobile ehlers-danlos syndrome: implications for research and clinical practice	36
Mental comorbidities in adolescents and young adults with juvenile idiopathic arthritis: an analysis of German nationwide health insurance data	32
The potential role of Colchicine in preventing coronary vascular disease in childhood‐onset lupus: a new view on an old drug	31
Predictive model based on gene and laboratory data for intravenous immunoglobulin resistance in Kawasaki disease in a Chinese population	27
‘The current mental health status of children and young people with JIA, and their wider family’: a charity partner collaboration survey	26
Growth and puberty in children with juvenile idiopathic arthritis	24
Monogenic systemic lupus erythematosus onset in a 13-year-old boy with Noonan like-syndrome: a case report and literature review	22
α2-fraction and haptoglobin as biomarkers for disease activity in oligo- and polyarticular juvenile idiopathic arthritis	21
Predictive value of Albumin-Bilirubin grade for intravenous immunoglobulin resistance in a large cohort of patients with Kawasaki disease: a prospective study	20
Clinical features and recurrence predictors of histiocytic necrotizing lymphadenitis in Chinese children	19
Effect of first-line biologic initiation on glucocorticoid exposure in children hospitalized with new-onset systemic juvenile idiopathic arthritis: emulation of a pragmatic trial using observational d	19
Infections and antibiotics during fetal life and childhood and their relationship to juvenile idiopathic arthritis: a prospective cohort study	19
Overlap syndrome in a 12-year-old girl with systemic lupus erythematosus and anti-oj antibody-positive polymyositis: a case report	17
Efficacy and safety of baricitinib in Japanese patients with autoinflammatory type I interferonopathies (NNS/CANDLE, SAVI, And AGS)	17
Profile of HLA-B27-positive enthesitis/spondylitis-related arthritis in Senegal, West Africa	17
IgA vasculitis nephritis clinical course and kidney biopsy – national study in children	17
Transition readiness in adolescents and young adults with chronic rheumatic disease in Oman: today’s needs and future challenges	17
Is an association of acro-osteolysis, bone fragility, and enchondromatosis a newfound disease caused by an amplification of PTHLH? A case report	16
Algorithmic approach in the diagnosis of pediatric uveitis	16
Colchicine treatment can be discontinued in a selected group of pediatric FMF patients	16
Effectiveness and safety of canakinumab in cryopyrin-associated periodic syndrome: a retrospective study in China	16

Prevalence of tissue transglutaminase antibodies and IgA deficiency are not increased in juvenile idiopathic arthritis: a case-control study	16
Anakinra and hepatotoxicity in pediatric rheumatology: a case series	16
Clinical observations on infliximab treatment of infantile onset Takayasu arteritis	15
Pain-coping scale for children and their parents: a cross-sectional study in children with musculoskeletal pain	15
Risk perception, well-being, depression and anxiety in children and adolescents with rheumatic diseases during the COVID-19 pandemic - results from the prospective multicenter KICK-COVID study in Germ	15
Haptoglobin in Juvenile Idiopathic Arthritis	14
Severe Raynaud’s phenomenon from ethosuximide raised concern over possible onset of systemic vasculitis: a case report	14
Musculoskeletal symptoms and their impact on health-related quality of life in chronic nonbacterial osteomyelitis patients	14
Duration of effect in treatment of methotrexate intolerance in juvenile idiopathic arthritis using Eye Movement Desensitization and Reprocessing (EMDR) can be improved by Bi-lateral Alternating Stimul	14
Distinct phenotypes of multisystem inflammatory syndrome in children: a cohort study	13
Reasons for canakinumab initiation among patients with periodic fever syndromes: a retrospective medical chart review from the United States	13
A pilot study of possible anti-inflammatory effects of the specific carbohydrate diet in children with juvenile idiopathic arthritis	13
Bilateral anterior and intermediate uveitis in SARS-CoV-2 associated multisystem inflammatory syndrome in a pediatric patient	13
Panniculitis with late onset enthesitis-related arthritis: a case report	13
The 4th NextGen therapies for SJIA and MAS: part 3 clinical trials in refractory SJIA: historic controls as an alternative to a withdrawal design study	12
Predictors of fibrogenesis in children with JIA: a single-center pilot study	12
Efficacy and safety of thalidomide in children with monogenic autoinflammatory diseases: a single-center, real-world-evidence study	12
Peripheral blood regulatory T cells and disease activity, quality of life, and outcomes in children with juvenile idiopathic arthritis	12
Vasculitis in a patient with mevalonate kinase deficiency (MKD): a case report	12
Proceedings of the 31st European Paediatric Rheumatology Congress: part 2	12
Chronic limping in childhood, what else other than juvenile idiopathic arthritis: a case series	12
Methotrexate inhibits BMP4 and abrogates the hypertrophic chondrocyte phenotype of synovial fibroblasts in juvenile idiopathic arthritis	12
“Online survey of COVID-19 immunization and infection in patients with systemic juvenile idiopathic arthritis and adult-onset still’s disease.”	12
Reverse complete heart block using transcutaneous pacing and repeated plasmapheresis in a neonate with lupus: a case report	12
Diffuse alveolar hemorrhage in children with trisomy 21	11
Revising the WHO Essential Medicines List for paediatric rheumatology	11
Impaired cardiorespiratory and neuromuscular fitness in children and adolescents with juvenile idiopathic arthritis: a cross-sectional case–control study in the era of biologic drug therapies	11
Capturing critical data elements in Juvenile Idiopathic Arthritis: initiatives to improve data capture	11
Clinical features, treatment, and outcomes of celiac-associated arthritis: a retrospective cohort study	11
Revising the WHO Essential Medicines List for paediatric rheumatology update	11
The successes and challenges of harmonising juvenile idiopathic arthritis (JIA) datasets to create a large-scale JIA data resource	10
Fecal microbiota in children with juvenile idiopathic arthritis treated with methotrexate or etanercept	10
Establishment and analysis of a novel diagnostic model for systemic juvenile idiopathic arthritis based on machine learning	10
Macrophage activation syndrome in juvenile dermatomyositis: a case report and a comprehensive review of the literature	10
Barriers to care in juvenile localized and systemic scleroderma: an exploratory survey study of caregivers’ perspectives	10
Baseline characteristics of children with juvenile dermatomyositis enrolled in the first year of the new Childhood Arthritis and Rheumatology Research Alliance registry	10
Glucose metabolism in systemic juvenile idiopathic arthritis	10
The assessment of bone health in children with juvenile idiopathic arthritis; comparison of different imaging-based methods	10
Paediatric autoimmune diseases with ELANE mutations associated with neutropenia	10
Disease relapse rate in children with autoimmune rheumatic diseases after COVID-19 infection and vaccination	9
Thrombotic thrombocytopenic purpura with juvenile systemic lupus erythematosus: successful treatment with caplacizumab and rituximab	9
Clinical features of Kawasaki disease initially mimicking retropharyngeal abscess: a retrospective analysis	9
Clinical characteristics and genetic analysis of A20 haploinsufficiency	9
The patient’s voice: a cross-sectional study of physical health and disability in juvenile idiopathic arthritis	9
A qualitative study of risk and resilience in young adult women with a history of juvenile-onset fibromyalgia	9
A quantitative comparison between the essential medicines for rheumatic diseases in children and young people in Africa and the WHO model list	9
Anti-SAE autoantibody-positive Japanese patient with juvenile dermatomyositis complicated with interstitial lung disease - a case report	9
Tofacitinib effectiveness in Blau syndrome: a case series of Chinese paediatric patients	9
The efficacy and safety of allogeneic stem cell transplantation in Mevalonate Kinase Deficiency	9
Increase in stress contributes to impaired jaw function in juvenile idiopathic arthritis: a two-year prospective study	9

Towards telehealth delivery in pediatric rheumatology practice	9
A20 haploinsufficiency in a neonate caused by a large deletion on chromosome 6q	9
Part 5: Allogeneic HSCT in refractory SJIA with lung disease; recent cases from centers in North America & Europe	9
Increasing the etanercept dose in a treat-to-target approach in juvenile idiopathic arthritis: does it help to reach the target? A post-hoc analysis of the BeSt for Kids randomised clinical trial	9
Developmentally appropriate transitional care during the Covid-19 pandemic for young people with juvenile-onset rheumatic and musculoskeletal diseases: the rationale for a position statement	9
Childhood-Onset ANCA- Associated Vasculitis: single center experience from Central California	9
Clinical characteristics and COVID-19 outcomes in a regional cohort of pediatric patients with rheumatic diseases	9
Outcomes of COVID-19 in a cohort of pediatric patients with rheumatic diseases	9
Implementation study of the CARRA Uveitis Consensus Treatment Plans: feasibility for clinical practice and applicability for research	8
Anasarca as the presenting symptom of juvenile dermatomyositis: a case series	8
Epidemiology and demographics of juvenile idiopathic arthritis in Africa and Middle East	8
Intravenous administration of anakinra in children with macrophage activation syndrome	8
Juvenile dermatomyositis: association between nail fold capillary end row loop– area under the curve– and disease damage indicators	8
Discontinuation of biologic DMARDs in non-systemic JIA patients: a scoping review of relapse rates and associated factors	8
Three cases of autoinflammatory disease with novel NLRC4 mutations, and the first mutation reported in the CARD domain of NLRC4 associated with autoinflammatory infantile enterocolitis (AIFEC)	8
Explaining juvenile idiopathic arthritis to paediatric patients using illustrations and easy-to-read texts: improvement of disease knowledge and adherence to treatment	8
Subtype frequency, demographic features, treatment and outcome of Juvenile Arthritis in one Centre in Abu Dhabi in the United Arab Emirates	8
The protective effect of COVID-19 vaccines on developing multisystem inflammatory syndrome in children (MIS-C): a systematic literature review and meta-analysis	8
Dutch patients, caregivers and healthcare professionals generate first nationwide research agenda for juvenile idiopathic arthritis	8
The relation between C-reactive protein and serum amyloid A in patients with autoinflammatory diseases	8
Patient with H syndrome, cardiogenic shock, multiorgan infiltration, and digital ischemia	8
Level and correlates of physical activity among children and adolescents with juvenile idiopathic arthritis compared to controls: results from a German nationwide prospective observational cohort stud	8
Prevalence of autoantibodies in patients with juvenile idiopathic arthritis: results from the German inception cohort ICON-JIA	8
Progressive, refractory macrophage activation syndrome as the initial presentation of anti-MDA5 antibody positive juvenile dermatomyositis: a case report and literature review	7
Towards a histological diagnosis of childhood small vessel CNS vasculitis	7
Musculoskeletal involvement in childhood leukemia: Characteristics and survival outcomes	7
Correction to: Heme oxygenase-1 deficiency presenting with interstitial lung disease and hemophagocytic flares	7
Role of ultrasound and inflammatory factors in the management of pediatric hip joint effusion	7
Tocilizumab reduces the unmanageable inflammatory reaction of a patient with Aicardi-Goutières syndrome type 7 during treatment with ruxolitinib	7
Disease evolution in systemic juvenile idiopathic arthritis: an international, observational cohort study through JIRcohort	7
In a large Juvenile Idiopathic Arthritis (JIA) cohort, concomitant celiac disease is associated with family history of autoimmunity and a more severe JIA course: a retrospective study	7
Meningococcal ACWY conjugate vaccine immunogenicity in adolescents with primary or secondary immune deficiencies, a prospective observational cohort study	7
Juvenile eosinophilic fasciitis: a single center case series	7
Touraine-Solente-Gole syndrome: pathogenic variant in SLCO2A1 presented with polyarthralgia and digital clubbing	7
Real-world psychosocial impact among patients with juvenile idiopathic arthritis and families in Spain	7
Evaluation of pediatric rheumatology telehealth satisfaction during the COVID-19 pandemic	7
Aicardi-Goutières syndrome type 6: report of ADAR variant and clinical outcome after ruxolitinib treatment in the neonatal period	7
Non-criteria antiphospholipid antibodies and pediatric rheumatic disease: a case series	7
Myeloid-related protein 8/14 in plasma and serum in patients with new-onset juvenile idiopathic arthritis in real-world setting in a single center	7
Biomarkers of lipid metabolism in patients with juvenile idiopathic arthritis: relationship with disease subtype and inflammatory activity	7
Health-related quality of life, continuity of care and patient satisfaction: long-term outcomes of former patients of the Tuebingen Transition Program (TTP) – a retrospective cohort study	7
Transition readiness among finnish adolescents with juvenile idiopathic arthritis	7
Priorities in Chronic nonbacterial osteomyelitis (CNO) – results from an international survey and roundtable discussions	7
Successful rituximab treatment for severe rapidly progressive interstitial lung disease with anti-MDA5 antibody-positive juvenile dermatomyositis: a case report and literature review	7
Correction: Importance of pediatric rheumatologists and transitional care for juvenile idiopathic arthritis-associated uveitis: a retrospective series of 9 cases	7
Mere coincidence or an association? Case of juvenile idiopathic arthritis in a patient with Klinefelter syndrome	7
Elevated serum IFN-γand IFN-γ/IL-6 ratio in Kikuchi-Fujimoto disease	7
TNFAIP3 mutation causing haploinsufficiency of A20 with a hemophagocytic lymphohistiocytosis phenotype: a report of two cases	7
Juvenile primary Fibromyalgia Syndrome: epidemiology, etiology, pathogenesis, clinical manifestations and diagnosis	7
Why so low? An unusual case of myositis in a child	7
Proceedings of the 27th European Paediatric Rheumatology Congress (PReS 2021)	7
Integrin α2 gene polymorphism is a risk factor of coronary artery lesions in Chinese children with Kawasaki disease	6
Knowledge about juvenile idiopathic arthritis-associated uveitis: more frequent reminders are associated with higher patient and family uveitis knowledge	6
Prevalence of spine pain among Tunisian children and adolescents and related factors	6
A novel mutation in early‐onset sarcoidosis/Blau syndrome: an association with Propionibacterium acnes	6
Unravelling the clinical heterogeneity of undefined recurrent fever over time in the European registries on Autoinflammation	6
Juvenile idiopathic arthritis in Jordan: single center experience	6
Reducing fatigue in pediatric rheumatic conditions: a systematic review	6
Immunoprofiling of active and inactive systemic juvenile idiopathic arthritis reveals distinct biomarkers: a single-center study	6
Single center clinical analysis of macrophage activation syndrome complicating juvenile rheumatic diseases	6
Long-term growth and final adult height outcome in childhood-onset systemic lupus erythematosus	6
Kawasaki disease complicated by peripheral artery thrombosis: a case report and literature review	6
Differences in rituximab use between pediatric rheumatologists and nephrologists for the treatment of refractory lupus nephritis and renal flare in childhood-onset SLE	6
Withdrawing biologics in non-systemic JIA: what matters to pediatric rheumatologists?	6
Resilience and its associations in children with Systemic Lupus Erythematosus and Juvenile Idiopathic Arthritis	6
The “Intermediate” CD14 + CD16 + monocyte subpopulation plays a role in IVIG responsiveness of children with Kawasaki disease	6
Delivery of paediatric rheumatology care: a survey of current clinical practice in Southeast Asia and Asia-Pacific regions	6
Pediatric rheumatology in Africa: thriving amidst challenges	6
Effect of exercise training on heath, quality of life, exercise capacity in juvenile idiopathic arthritis: a meta-analysis of randomized controlled trials	6
Identification of key biomarkers in RF-negative polyarticular and oligoarticular juvenile idiopathic arthritis by bioinformatic analysis	6
Community poverty level influences time to first pediatric rheumatology appointment in Polyarticular Juvenile Idiopathic Arthritis	6
Translating research into practice—implementation recommendations for pediatric rheumatology; Proceedings of the childhood arthritis and rheumatology research alliance 2020 implementation science retr	6
Beneficial effects of anti-apolipoprotein A-2 on an animal model for coronary arteritis in Kawasaki disease	6
Lung infection or inflammation-a puzzling case of MDA-5 associated juvenile dermatomyositis	6
Kawasaki disease with an asymptomatic reversible splenial lesion	6
Treatment of thrombosis in KD Patients using tissue plasminogen activator: a single center study	6
Tumor necrosis factor inhibitors for pediatric patients with SAPHO syndrome associated with acne conglobata	6
Bridging gaps: a qualitative inquiry on improving paediatric rheumatology care among healthcare workers in Kenya	6
A case series on recurrent and persisting IgA vasculitis (Henoch Schonlein purpura) in children	6
Involvement of the systemic microcirculation in pediatric uveitis	6