Annals of Neurology

Papers
(The TQCC of Annals of Neurology is 13. The table below lists those papers that are above that threshold based on CrossRef citation counts [max. 250 papers]. The publications cover those that have been published in the past four years, i.e., from 2022-01-01 to 2026-01-01.)
ArticleCitations
222
Reply to “Urinary α‐Synuclein for Parkinson's Detection: Key Limitations and Future Directions”194
Issue Information138
128
Efficacy and Safety of Ofatumumab Treatment for Anti‐NMDA Receptor Autoimmune Encephalitis (OFFAE): A Prospective, Multicenter Cohort Study124
Elevated Cerebrospinal Fluid Ubiquitin Carboxyl‐Terminal Hydrolase Isozyme L1 in Asymptomatic C9orf72 Hexanucleotide Repeat Expansion Carriers104
Vertebral Artery Pseudoaneurysm: Novel Marker of Bow Hunter's Syndrome99
HLA Associations of Intrathecal IgG Production against Specific Viruses in Multiple Sclerosis99
98
Annals of Neurology: Volume 97, Number 1, January 202594
Carotid Stent Fracture89
Microneurography Reveals Unmyelinated Small Nerve Fiber Dysfunction in Long COVID88
Cerebrospinal Fluid Flow in Patients with Huntington's Disease83
Network Localization of Awareness in Visual and Motor Anosognosia82
Furthering Female Faculty: An American Neurological Association/Association of University Professors of Neurology Perspective81
A Letter Concerning a Role for Blood–Brain Barrier Dysfunction in Delirium following Noncardiac Surgery in Older Adults81
Interactions between High Seroreactivity to Human Herpes Virus 6A and Epstein–Barr Virus in MS Development: A Presymptomatic Case–Control Study81
Supratentorial Lymphocytic Inflammation with Parenchymal Perivascular Enhancement Responsive to Steroids: A Potentially Overlooked Diagnosis79
Association of Retromer Deficiency and Tau Pathology in Down Syndrome79
Septin‐5 and ‐7‐IgGs: Neurologic, Serologic, and Pathophysiologic Characteristics76
Epidemiology, Survival, and Clinical Characteristics of Inclusion Body Myositis76
Biological Age Acceleration and Motoric Cognitive Risk Syndrome75
Before, during, and after: An Argument for Safety and Improved Outcome of Thrombolysis in Acute Ischemic Stroke with Direct Oral Anticoagulant Treatment73
Management of Cerebral Venous Thrombosis Due to Adenoviral COVID‐19 Vaccination66
The Use of Antihypertensive Medication and In Vivo Alzheimer's Disease Pathology62
Prevalence of Cerebral Amyloid Angiopathy and Associated Risk of Subsequent Ischemic and Hemorrhagic Stroke and Mortality in a Nationwide Cohort62
Cortical Microhemorrhage Presentation of Small Vessel Primary Angiitis of the Central Nervous System62
A Managed Care System with Telemedicine Support for Neurological Emergencies61
Frailty across Neurological Diseases: Why Sex and Gender Matter60
MS ‐Driven Metabolic Alterations Are Recapitulated in iPSC ‐Derived Astrocytes60
Probabilistic Mapping Reveals Optimal Stimulation Site in Essential Tremor58
Diet, Pace of Biological Aging, and Risk of Dementia in the Framingham Heart Study57
A Role for Insulin‐like Growth Factor 1 in the Generation of Epileptic Spasms in a murine model56
Staufen Impairs Autophagy in Neurodegeneration56
Guanylate Kinase 1 Deficiency: A Novel and Potentially Treatable Mitochondrial DNA Depletion/Deletions Disease55
Plasma Metabolites Link Dietary Patterns to Stroke Risk55
Blood Pressure after Successful Endovascular Therapy: A Systematic Review and Meta‐Analysis of Randomized Control Trials53
Dysregulation of Gut Microbiota‐Derived Neuromodulatory Amino Acid Metabolism in Human Immunodeficiency Virus‐Associated Neurocognitive Disorder: An Integrative Metagenomic and Metabolomic 52
Effect of Imaging Markers on Reperfusion Therapy in Basilar Artery Occlusion52
Severity of GNAO1‐Related Disorder Correlates with Changes in G‐Protein Function51
Suvorexant Acutely Decreases Tau Phosphorylation and Aβ in the Human CNS50
Issue Information49
Annals of Neurology: Volume 94, Number S30, September 202349
Cover Image49
Longitudinal Imaging Biomarkers Correlate with Progressive Motor Deficit in the Mouse Model of Charlevoix‐Saguenay Ataxia48
MEK Pathway Inhibitor‐Mediated Response in BRAF V600‐Mutant Melanoma with Brain Parenchymal and Leptomeningeal Metastases47
Sports Concussion and Category Mistakes47
Issue Information46
Correction: Regional Glymphatic Abnormality in Behavioral Variant Frontotemporal Dementia46
Trials for Slowly Progressive Neurogenetic Diseases Need Surrogate Endpoints45
Sensorimotor Cortex High Frequency Oscillations Characterize Motor Symptom Severity during Deep Brain Stimulation Surgery for Parkinson's Disease45
Tenascin‐R Autoimmunity: Isolated Tremor Reversed with Immunotherapy45
Micro‐Doses of DNP Preserve Motor and Muscle Function with a Period of Functional Recovery in Amyotrophic Lateral Sclerosis Mice44
Development of Parkinson Disease and Its Relationship with Incidentally Discovered White Matter Disease and Covert Brain Infarction in a Real‐World Cohort44
Intravenous Thrombolysis in Patients Taking Direct Oral Anticoagulation Treatment Before Stroke Onset: Results from the Safe Implementations of Treatments in Stroke International Stroke Registry44
Correction: GATA1‐Mediated Transcriptional Regulation of the γ‐Secretase Activating Protein Increases Aβ Formation in Down Syndrome44
Cross‐Sectional FDG in Down Syndrome and Autosomal Dominant Alzheimer's Disease44
GGC Repeat Expansion of RILPL1 is Associated with Oculopharyngodistal Myopathy43
Regional Brain Metabolism across the Alzheimer's Disease Continuum in Down Syndrome43
Clarifying the Moderating Role of Socioeconomic Status on Amyloid‐Related Gray Matter Atrophy43
Illusions of Self‐Motion during Magnetic Resonance‐Guided Focused Ultrasound Thalamotomy for Tremor43
A Combined Panel of Salivary Biomarkers in de novo Parkinson's Disease42
GABRA1‐Related Disorders: From Genetic to Functional Pathways42
RAN Translation of C9orf72‐Related Dipeptide Repeat Proteins in Zebrafish Recapitulates Hallmarks of Amyotrophic Lateral Sclerosis and Identifies Hypothermia as a Therap41
Visual Features in Stereo‐Electroencephalography to Predict Surgical Outcome: A Multicenter Study41
Choroid Plexus Enlargement Exacerbates White Matter Hyperintensity Growth through Glymphatic Impairment40
Ultrastructural Axon–Myelin Unit Alterations in Multiple Sclerosis Correlate with Inflammation40
Improving Early Recognition of Treatment‐Responsive Causes of Rapidly Progressive Dementia: The STAM3P Score40
APOE2 Exacerbates TDP‐43 Related Toxicity in the Absence of Alzheimer Pathology40
Reply to “ AI: Need for Comparative Studies in Complex Neurologic Diagnosis”40
Dopamine Transporter Imaging as Objective Monitoring Biomarker in Parkinson's Disease39
Association of Seizure Control with Mortality, Cognition, and Function in People With Dementia39
NINDS Corner: The Helping to End Addiction Long‐Term Initiative and Pain Neurology38
Issue Information37
36
Bilateral Hearing Loss Caused by Inferior Collicular Infarction36
Is there an Association between Tuber Involvement of the Fusiform Face Area in Autism Diagnosis?36
Reply to “Letter on Multiple Acyl‐Coenzyme A Dehydrogenase Deficiency Is Associated with Sertraline Use”36
Issue Information35
Reply to “Is There an Association between Tuber Involvement of the Fusiform Face Area in Autism Diagnosis?”35
Brain Iron Dysregulation in Iron Deficiency Anemia‐Related Restless Leg Syndrome Revealed by Neuron‐Derived Extracellular Vesicles: A Case–Control Study35
Reply to “Clinical Relevance of Genetic Variants in Juvenile Stroke Patients: A Plea for a Precise Classification”35
Issue Information35
Reply to “Chance Bias Arising from TSC2 Mutation Imbalance in the PREVeNT Trial”35
Use of FDGPET in Balamuthia mandrillaris34
Heart Rate Profiles During Exercise and Incident Parkinson's Disease34
Comment on Clinical, Prognostic, and Longitudinal Functional and Neuropsychological Features of West Nile Virus Neuroinvasive Disease in the United States: A Systematic Review and Meta‐Analysis34
Autoimmune Glial Fibrillary Acidic Protein Astrocytopathy Is Associated with HLA‐A*3303 and HLA‐DPB1*050134
Compensated Hypogonadism Identified in Males with Cluster Headache: A Prospective Case‐Controlled Study34
Bleeding Risk of Dual Antiplatelet Therapy after Minor Stroke or Transient Ischemic Attack34
Trigeminal Trophic Syndrome from Lateral Medullary Stroke33
Uncovering Image‐Driven Subtypes with Distinct Pathology and Clinical Course in Autopsy‐Confirmed Four Repeat Tauopathies33
Neocortical LBD in Women and Episodic Memory Decline in Men: Clarifying Sex Effects33
33
Recessive Variants in PIGG Cause a Motor Neuropathy with Variable Conduction Block, Childhood Tremor, and Febrile Seizures: Expanding the Phenotype33
Nocturnal Pulse Event Frequency Is Reduced in Multiple System Atrophy33
High‐Dose Pulse Glucocorticoid Treatment Prevents White Matter Spinal Cord Pseudoatrophy in Newly Diagnosed Multiple Sclerosis33
Greater Diffusion Restriction in White Matter in Preclinical Alzheimer Disease33
Extending the Interpretation of Biomarker Dynamics in SOD1ALS Proteomics32
Automated Neuroprognostication Via Machine Learning in Neonates with Hypoxic‐Ischemic Encephalopathy32
Prophylactic Fetal Creatine Supplementation Improves Post‐Asphyxial EEG Recovery and Reduces Seizures in Fetal Sheep: Implications for Hypoxic–Ischemic Encephalopathy32
Actigraphy Enables Home Screening of Rapid Eye Movement Behavior Disorder in Parkinson's Disease32
Histopathological Correlates of Lobar Microbleeds in False‐Positive Cerebral Amyloid Angiopathy Cases32
Genome‐Wide Analysis of Structural Variants in Parkinson Disease32
Determinants of Infarct Core Growth During Inter‐hospital Transfer for Thrombectomy32
Neuroimaging Biomarkers for Friedreich Ataxia: A Cross‐Sectional Analysis of the TRACKFA Study32
Responsiveness of the Scale for the Assessment and Rating of Ataxia and Natural History in 884 Recessive and Early Onset Ataxia Patients32
Stage‐Dependent Biomarker Changes in Spinocerebellar Ataxia Type 331
In Memoriam: Arthur Knight Asbury, MD (1928–2022)31
Fighting Amyotrophic Lateral Sclerosis by Protecting the Liver? A Prospective Cohort Study31
COVID‐19‐Associated Critical Illness Myopathy with Direct Viral Effects31
Signs of Cortical Inflammation in Migraine Measured with Quantitative Magnetic Resonance Imaging: A Registry for Migraine (REFORM) Study31
Correction: Decreased Cerebrospinal Fluid Amyloid β 38, 40, 42, and 43 Levels in Sporadic and Hereditary Cerebral Amyloid Angiopathy31
30
Issue Information30
ANA Investigates: Atrial Fibrillation after Stroke30
Issue Information – TOC30
Pivotal Role of Slitrk1 in Adult Striatal Cholinergic Neurons in Mice: Implication in Tourette Syndrome30
Issue Information30
Search Strategies for Alzheimer Protector Genes29
Reply to “VAERS Could Miss or Misinterpret Neurological Side Effects of COVID Vaccinations”29
ANA Podcasts & Webinars: Genetics of Epilepsy29
Disease‐Modifying Drugs Extend Survival in Hereditary Transthyretin Amyloid Polyneuropathy29
SRPK3 Is Essential for Cognitive and Ocular Development in Humans and Zebrafish, Explaining X‐Linked Intellectual Disability28
Adolescent Headache Due to Congenital Pelvic/Sacral Vascular Malformation28
Happy 75th National Institute of Neurological Disorders and Stroke28
Comparative Safety of Antiseizure Medication Monotherapy for Major Malformations28
Elevated Risk of Cerebral Arteriovenous Malformation Rupture during Pregnancy and Puerperium28
Epstein–Barr Virus, Lower Vitamin D, Low Sun Exposure, and HLADRB1*1501 Risk Variant Share Common Epigenetic Pathways Leading to Multiple Sclerosis Onset28
CADASIL Affects Multiple Aspects of Cerebral Small Vessel Function on 7T‐MRI28
Reply to “The Role of EEG in Predicting Post‐Stroke Seizures and an Updated Prognostic Model ( SeLECT 28
Extra Movements in Healthy People: Challenging the Definition and Diagnostic Practice of Tic Disorders27
Evaluation of Soluble Colony Stimulating Factor 1 Receptor (CSF1R) in Peripheral Blood as a Diagnostic Marker of CSF1R‐Related Disorder (CSF1RRD) in a Muri27
Ultra‐Low Level Somatic Mutations and Structural Variations in Focal Cortical Dysplasia Type II27
Correction to “Protective Effects of Socioeconomic Status and Lifestyle on Amyloid‐ and White Matter Hyperintensity‐Related Longitudinal Brain Atrophy and Cognitive Decline”27
Effect of Cumulative Exposure to Ocrelizumab on Memory B‐Cell Repopulation Dynamics in Multiple Sclerosis27
Subcortical Volumes as Early Predictors of Fatigue in Multiple Sclerosis27
Issue Information26
Application of the Amyloid/Tau/Neurodegeneration Framework in Cognitively Intact Adults: The CABLE Study26
Risk of Multiple Sclerosis in People Living with HIV: An International Cohort Study26
Spoken Language Alterations can Predict Phenoconversion in Isolated Rapid Eye Movement Sleep Behavior Disorder: A Multicenter Study26
Cerebral Small Vessel Disease Progression Increases Risk of Incident Parkinsonism26
Smouldering‐Associated Worsening in Multiple Sclerosis: An International Consensus Statement on Definition, Biology, Clinical Implications, and Future Directions26
Cortical Correlates of Gait Compensation Strategies in Parkinson Disease26
Issue Information25
NORSE, FIRES, and a Polygenic Trickle of Autoimmunity25
High Levels of Perivascular Inflammation and Active Demyelinating Lesions at Time of Death Associated with Rapidly Progressive Multiple Sclerosis Disease Course: A Retrospective Postmortem Cohort Stud25
Annals of Neurology: Volume 95, Number 4, April 202425
Correction to Lyden P, Pryor KE, Coffey CS, et al. Final results of the RHAPSODY trial: a multi‐center, phase 2 trial using a continual reassessment method to determine the safety and toler25
Network Localization of Pediatric Lesion‐Induced Dystonia25
Disease Progression in Charcot–Marie–Tooth Disease Related to MPZ Mutations: A Longitudinal Study25
Annual Report from the Editor‐in‐Chief (2024)25
Annals of Neurology: Volume 96, Number 2, August 202425
Sex Differences in Trends in Stroke Recurrence and Postrecurrence Mortality 2000–2020: Population‐Based Brain Attack Surveillance in Corpus Christi Project25
Charcot Joint25
Salivary CGRP and Erenumab Treatment Response: Towards Precision Medicine in Migraine24
Brainstem Ischemic Syndrome in NF2‐Related Schwannomatosis24
Temporal Pattern of Cortical Hypoxia in Multiple Sclerosis and Its Significance on Neuropsychological and Clinical Measures of Disability24
Internal Carotid Artery Pseudoaneurysm and Unilateral Vocal Cord Paralysis Secondary to Parapharyngeal Space Abscess24
Systemic Metabolic Alteration Dependent on the Thyroid‐Liver Axis in Early PD24
Cinematic Rendering of Extracranial to Intracranial Arterial Bypass24
A Carotid Web with Atherosclerotic Plaque24
Prediction of Cognitive Heterogeneity in Parkinson's Disease: A 4‐Year Longitudinal Study Using Clinical, Neuroimaging, Biological and Electrophysiological Biomarkers24
Emerging Management Challenges Posed by Atrial Fibrillation Detected After Stroke24
AAV9‐DARS2 Gene Therapy Rescues Phenotype in Leukoencephalopathy with Brainstem and Spinal Cord Involvement and Lactate Elevation Patient Cells and Neuronal Dars2 D24
Risk‐Based EEG Allocation: The Next Step for SeLECTEEG23
Polygenic Resistance to Blood Pressure Treatment and Stroke Risk: Insights from the All of Us Research Program23
Activated Wake Systems in Narcolepsy Type 123
Trametinib in Adults with Neurofibromatosis Type 1‐Related Symptomatic Plexiform Neurofibromas23
Inflammation in Cerebral Amyloid Angiopathy‐Related Transient Focal Neurological Episodes23
“Don't Throw the Baby out with the Bathwater”23
Reply to “Genetic Risk, Drug Regimens, and the Limits of Equitable Translation”23
Social Health and Cognitive Change in Old Age: Role of Brain Reserve23
Intravenous Thrombolysis with Tenecteplase for the Treatment of Acute Ischemic Stroke23
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22
MuSK‐Myasthenia Gravis and Cancer22
Enhancement of Glutamate Uptake as Novel Antiseizure Approach: Preclinical Proof of Concept22
Limbic Stimulation Drives Mania in STN‐DBS in Parkinson Disease: A Prospective Study22
Annals of Neurology: Volume 92, Number 3, September 202222
Vessel Wall Imaging of a Carotid Web22
Disease Characteristics and Treatments Associated with Outcome in Primary Angiitis of the Central Nervous System —A Multicenter Cohort Study in 163 P22
Cinematic Rendering of Twig‐Like Middle Cerebral Artery22
Reply to “Myelin Oligodendrocyte Glycoprotein Antibody‐Positive Patients Meeting the 2017 McDonald Criteria for Multiple Sclerosis: Challenges in Diagnosis and Treatment Decisions”22
De Novo Missense Variants in SLC32A1 Cause a Developmental and Epileptic Encephalopathy Due to Imp22
Diagnosing Epilepsy with Normal Interictal EEG Using Dynamic Network Models22
Role of the Exposome in Neurodegenerative Disease: Recent Insights and Future Directions22
Issue Information22
Fostering Academia‐Industry Partnerships to Facilitate Therapeutic Discoveries in Neurology: The Role of ANA as a Catalyst22
MOG‐IgG‐Associated Bilateral Optic Neuritis in Temporal Relation to Monkeypox Vaccination22
22
Neutrophils Are Associated with Higher Risk of Incident Amyotrophic Lateral Sclerosis in a BMI‐ and Age‐Dependent Manner22
Association of Apolipoprotein E ɛ4 Allele with Enlarged Perivascular Spaces22
Decoding the Clinical Features that Associate with Progression, Causes, and Outcomes in Patients with Suspected Rapidly Progressive Dementia21
21
Longitudinal Alterations of Cerebral Blood Flow in High‐Contact Sports21
Autosomal Recessive Cerebellar Ataxias: Translating Genes to Therapies21
Re‐Emergence of Poliovirus in the United States: Considerations and Implications21
Myelin Oligodendrocyte Glycoprotein Antibody‐Positive Patients Meeting the 2017 McDonald Criteria for Multiple Sclerosis: Challenges in Diagnosis and Treatment Decisions21
APOE Antibody Inhibits Aβ‐Associated Tau Seeding and Spreading in a Mouse Model20
Levodopa Impairs the Energy Metabolism of the Basal Ganglia In Vivo20
Cognitive Effects of Deep Brain Stimulation in GBA‐Related Parkinson Disease20
Divergent Causes and Convergent Mechanisms of SUDEP20
Resilience to Endoplasmic Reticulum Stress Mitigates Membrane Hyperexcitability Underlying Late Disease Onset in a Murine Model of SCA620
Neuroprotection of Low‐Frequency Repetitive Transcranial Magnetic Stimulation after Ischemic Stroke in Rats20
Microglial and Astrocytic Responses in the Human Midcingulate Cortex in Huntington's Disease20
Reply to “Reassessing the Impact of Endovascular Thrombectomy on Cerebral Edema and Functional Outcomes”20
Clinical and Molecular Genetic Characterization of Landau Kleffner Syndrome: An Observational Cohort and Experimental Study20
Intact HIV Proviruses Persist in the Brain Despite Viral Suppression with ART20
Phase 1 Evaluation of Elezanumab (Anti–Repulsive Guidance Molecule A Monoclonal Antibody) in Healthy and Multiple Sclerosis Participants20
Pathogenic Variants in RNU2‐2 , a Non‐coding Spliceosomal RNA , Cause a Distinctive Developmental and 20
Proteomic Indicators of Health Predict Alzheimer's Disease Biomarker Levels and Dementia Risk19
Annals of Neurology: Volume 95, Number 3, March 202419
Timing of Changes in Alzheimer's Disease Plasma Biomarkers as Assessed by Amyloid and Tau PET Clocks19
Spasticity Predicts Motor Recovery for Patients with Subacute Motor Complete Spinal Cord Injury19
Cluster Headache Genomewide Association Study and Meta‐Analysis Identifies Eight Loci and Implicates Smoking as Causal Risk Factor19
The Starry Cortex of Aβ‐Related Angiitis19
Mutations in CLCN6 as a Novel Genetic Cause of Neuronal Ceroid Lipofuscinosis in Patients and a Murine Model19
Longitudinal Retinal Changes in MOGAD19
Life‐Limiting Peripheral Organ Dysfunction in Feline Sandhoff Disease Emerges after Effective CNS Gene Therapy19
Presynaptic Dopaminergic Imaging Characterizes Patients with REM Sleep Behavior Disorder Due to Synucleinopathy19
Networks Underlie Temporal Onset of Dysplasia‐Related Epilepsy: A MELD Study19
Annals of Neurology: Volume 93, Number 4, April 202319
Characterizing Frontal Lobe Seizure Semiology in Children19
Disparate Dementia Risk Factors Are Associated with Cognitive Impairment and Rates of Decline in African Americans19
Minimally Invasive Surgery Versus Open Craniotomy With Clot Evacuation After Intracerebral Hemorrhage19
Blood‐Based Proteomics for Adult‐Onset Focal Dystonias19
Pragmatic Clinical Trials in Neurology19
AI in Neurology: Everything, Everywhere, All at Once Part 3: Surveillance, Synthesis, Simulation, and Systems19
Reply to “Type I IFN Signature in NOTCH1‐Related Leukoencephalopathy”19
Proteomics and the Risk of Incident Embolic and Thrombotic Stroke18
Reply to “Letter to the Editor, Regarding ‘Intravenous Thrombolysis in Patients Taking Direct Oral Anticoagulation Treatment Before Stroke Onset: Results from the Safe Implementations of Treatments in18
Obesity and Multiple Sclerosis Severity: A Mendelian Randomization Study18
Eligibility Rates among Racially and Ethnically Diverse US Participants in Phase 2 and Phase 3 Placebo‐Controlled, Double‐Blind, Randomized Trials of Lecanemab and Elenbecestat in Early Alz18
Inhibition of Bone Morphogenetic Protein Signaling Prevents Tau Pathology in iPSC Derived Neurons and PS19 Mice18
Cost‐Effectiveness of Endovascular Thrombectomy in Patients with Large Ischemic Stroke18
Perimesencephalic Hemorrhage from A Superior Cerebellar Artery Dissection18
Amyloid‐Related Imaging Abnormalities in the DIAN‐TU‐001 Trial of Gantenerumab and Solanezumab: Lessons from a Trial in Dominantly Inherited Alzheimer Disease18
Clinically Meaningful Magnetic Resonance Endpoints Sensitive to Preataxic Spinocerebellar Ataxia Types 1 and 318
Association of Mismatch Profiles and Clinical Outcome from Endovascular Therapy in Large Infarct: A Post‐Hoc Analysis of the ANGELASPECT Trial17
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Mapping Molecular Pathways of Multiple Sclerosis: A Gene Prioritization and Network Analysis of White Matter Pathology Transcriptomics17
Issue Information17
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Neurological Performance is not Evolutionary Fitness in Huntington's Disease17
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Annals of Neurology: Volume 91, Number 2, February 202217
Annals of Neurology: Volume 96, Number 5, November 202417
Clinical Relevance of ‘Cap’ and ‘Track’ Development after Recent Small Subcortical Infarct17
Divergent Associations of Slow‐Wave Sleep versus Rapid Eye Movement Sleep with Plasma Amyloid‐Beta17
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