Annals of Neurology

Papers
(The TQCC of Annals of Neurology is 12. The table below lists those papers that are above that threshold based on CrossRef citation counts [max. 250 papers]. The publications cover those that have been published in the past four years, i.e., from 2021-05-01 to 2025-05-01.)
ArticleCitations
Annals of Neurology: Volume 90, Number S27, October 2021172
Association of Retromer Deficiency and Tau Pathology in Down Syndrome163
Cerebrospinal Fluid Flow in Patients with Huntington's Disease140
Supratentorial Lymphocytic Inflammation with Parenchymal Perivascular Enhancement Responsive to Steroids: A Potentially Overlooked Diagnosis127
A Managed Care System with Telemedicine Support for Neurological Emergencies117
Dysregulation of Gut Microbiota‐Derived Neuromodulatory Amino Acid Metabolism in Human Immunodeficiency Virus‐Associated Neurocognitive Disorder: An Integrative Metagenomic and Metabolomic 113
Issue Information108
Hypoparathyroidism Associated with Vascular Centrum Semiovale Calcifications100
A Letter Concerning a Role for Blood–Brain Barrier Dysfunction in Delirium following Noncardiac Surgery in Older Adults97
Furthering Female Faculty: An American Neurological Association/Association of University Professors of Neurology Perspective94
Blood Pressure after Successful Endovascular Therapy: A Systematic Review and Meta‐Analysis of Randomized Control Trials93
Interactions between High Seroreactivity to Human Herpes Virus 6A and Epstein–Barr Virus in MS Development: A Presymptomatic Case–Control Study92
Cortical Microhemorrhage Presentation of Small Vessel Primary Angiitis of the Central Nervous System91
Elevated Cerebrospinal Fluid Ubiquitin Carboxyl‐Terminal Hydrolase Isozyme L1 in Asymptomatic C9orf72 Hexanucleotide Repeat Expansion Carriers88
The Use of Antihypertensive Medication and In Vivo Alzheimer's Disease Pathology88
HLA Associations of Intrathecal IgG Production against Specific Viruses in Multiple Sclerosis88
Issue Information83
Human Brain Resilience: A Call to Action83
Before, during, and after: An Argument for Safety and Improved Outcome of Thrombolysis in Acute Ischemic Stroke with Direct Oral Anticoagulant Treatment76
Carotid Stent Fracture75
Annals of Neurology: Volume 97, Number 1, January 202575
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Efficacy and Safety of Ofatumumab Treatment for Anti‐NMDA Receptor Autoimmune Encephalitis (OFFAE): A Prospective, Multicenter Cohort Study70
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Biological Age Acceleration and Motoric Cognitive Risk Syndrome67
Speech Biomarkers in Rapid Eye Movement Sleep Behavior Disorder and Parkinson Disease67
Guanylate Kinase 1 Deficiency: A Novel and Potentially Treatable Mitochondrial DNA Depletion/Deletions Disease67
Polygenic Risk Score for Alzheimer's Disease in Caribbean Hispanics63
Diet, Pace of Biological Aging, and Risk of Dementia in the Framingham Heart Study63
Network Localization of Awareness in Visual and Motor Anosognosia62
Septin‐5 and ‐7‐IgGs: Neurologic, Serologic, and Pathophysiologic Characteristics60
Management of Cerebral Venous Thrombosis Due to Adenoviral COVID‐19 Vaccination58
Vertebral Artery Pseudoaneurysm: Novel Marker of Bow Hunter's Syndrome58
Effect of Imaging Markers on Reperfusion Therapy in Basilar Artery Occlusion57
Staufen Impairs Autophagy in Neurodegeneration55
MS‐Driven Metabolic Alterations Are Recapitulated in iPSC‐Derived Astrocytes55
Epidemiology, Survival, and Clinical Characteristics of Inclusion Body Myositis53
Suvorexant Acutely Decreases Tau Phosphorylation and Aβ in the Human CNS52
Plasma Metabolites Link Dietary Patterns to Stroke Risk50
Severity of GNAO1‐Related Disorder Correlates with Changes in G‐Protein Function49
A Role for Insulin‐like Growth Factor 1 in the Generation of Epileptic Spasms in a murine model48
Probabilistic Mapping Reveals Optimal Stimulation Site in Essential Tremor48
Sports Concussion and Category Mistakes47
Annals of Neurology: Volume 94, Number S30, September 202346
Annals of Neurology: Volume 90, Number S26, September 202145
Reply to “Core Penumbral Mismatch: An Independent Predictor of Stroke Poorer Outcome”45
Cover Image44
Improving Early Recognition of Treatment‐Responsive Causes of Rapidly Progressive Dementia: The STAM3P Score44
Issue Information43
GABRA1‐Related Disorders: From Genetic to Functional Pathways43
A Combined Panel of Salivary Biomarkers in de novo Parkinson's Disease43
GGC Repeat Expansion of RILPL1 is Associated with Oculopharyngodistal Myopathy43
Micro‐Doses of DNP Preserve Motor and Muscle Function with a Period of Functional Recovery in Amyotrophic Lateral Sclerosis Mice42
Illusions of Self‐Motion during Magnetic Resonance‐Guided Focused Ultrasound Thalamotomy for Tremor42
Association of Seizure Control with Mortality, Cognition, and Function in People With Dementia42
APOE2 Exacerbates TDP‐43 Related Toxicity in the Absence of Alzheimer Pathology42
Subicular Caspase‐1 Contributes to Pharmacoresistance in Temporal Lobe Epilepsy42
Intravenous Thrombolysis in Patients Taking Direct Oral Anticoagulation Treatment Before Stroke Onset: Results from the Safe Implementations of Treatments in Stroke International Stroke Registry40
ANA Investigates: Tenecteplase40
RAN Translation of C9orf72‐Related Dipeptide Repeat Proteins in Zebrafish Recapitulates Hallmarks of Amyotrophic Lateral Sclerosis and Identifies Hypothermia as a Therapeutic Strategy39
Tenascin‐R Autoimmunity: Isolated Tremor Reversed with Immunotherapy39
Correction: GATA1‐Mediated Transcriptional Regulation of the γ‐Secretase Activating Protein Increases Aβ Formation in Down Syndrome39
MEK Pathway Inhibitor‐Mediated Response in BRAF V600‐Mutant Melanoma with Brain Parenchymal and Leptomeningeal Metastases39
Correction: Regional Glymphatic Abnormality in Behavioral Variant Frontotemporal Dementia39
Regional Brain Metabolism across the Alzheimer's Disease Continuum in Down Syndrome38
Development of Parkinson Disease and Its Relationship with Incidentally Discovered White Matter Disease and Covert Brain Infarction in a Real‐World Cohort38
Dopamine Transporter Imaging as Objective Monitoring Biomarker in Parkinson's Disease38
Preservation of Brain Activity in Unresponsive Patients Identifies MCS Star37
Choroid Plexus Enlargement Exacerbates White Matter Hyperintensity Growth through Glymphatic Impairment36
Trials for Slowly Progressive Neurogenetic Diseases Need Surrogate Endpoints36
Longitudinal Imaging Biomarkers Correlate with Progressive Motor Deficit in the Mouse Model of Charlevoix‐Saguenay Ataxia36
Issue Information35
Annals of Neurology: Volume 90, Number 3, September 202135
Neuroimaging Biomarkers for Friedreich Ataxia: A Cross‐Sectional Analysis of the TRACKFA Study35
Ultrastructural Axon–Myelin Unit Alterations in Multiple Sclerosis Correlate with Inflammation35
Bleeding Risk of Dual Antiplatelet Therapy after Minor Stroke or Transient Ischemic Attack34
Compensated Hypogonadism Identified in Males with Cluster Headache: A Prospective Case‐Controlled Study34
Foslevodopa/Foscarbidopa: A New Subcutaneous Treatment for Parkinson's Disease34
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Reply to “Clinical Relevance of Genetic Variants in Juvenile Stroke Patients: A Plea for a Precise Classification”34
Typical Radiological Features of a Rare Lateral Ventricular Liponeurocytoma34
Genome‐Wide Analysis of Structural Variants in Parkinson Disease33
Autoimmune Glial Fibrillary Acidic Protein Astrocytopathy Is Associated with HLA‐A*3303 and HLA‐DPB1*050133
Seizures after Ischemic Stroke: A Matched Multicenter Study33
Stage‐Dependent Biomarker Changes in Spinocerebellar Ataxia Type 333
Brain Iron Dysregulation in Iron Deficiency Anemia‐Related Restless Leg Syndrome Revealed by Neuron‐Derived Extracellular Vesicles: A Case–Control Study33
Signs of Cortical Inflammation in Migraine Measured with Quantitative Magnetic Resonance Imaging: A Registry for Migraine (REFORM) Study32
Greater Diffusion Restriction in White Matter in Preclinical Alzheimer Disease32
NINDS Corner: The Helping to End Addiction Long‐Term Initiative and Pain Neurology32
Responsiveness of the Scale for the Assessment and Rating of Ataxia and Natural History in 884 Recessive and Early Onset Ataxia Patients32
Automated Neuroprognostication Via Machine Learning in Neonates with Hypoxic‐Ischemic Encephalopathy31
Bilateral Hearing Loss Caused by Inferior Collicular Infarction31
COVID‐19‐Associated Critical Illness Myopathy with Direct Viral Effects31
Fighting Amyotrophic Lateral Sclerosis by Protecting the Liver? A Prospective Cohort Study31
Actigraphy Enables Home Screening of Rapid Eye Movement Behavior Disorder in Parkinson's Disease31
Determinants of Infarct Core Growth During Inter‐hospital Transfer for Thrombectomy31
Issue Information31
Investigation of Autosomal Genetic Sex Differences in Parkinson's Disease31
Reply to “Chance Bias Arising from TSC2 Mutation Imbalance in the PREVeNT Trial”30
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Issue Information30
Is there an Association between Tuber Involvement of the Fusiform Face Area in Autism Diagnosis?30
Trigeminal Trophic Syndrome from Lateral Medullary Stroke30
Nocturnal Pulse Event Frequency Is Reduced in Multiple System Atrophy30
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Prophylactic Fetal Creatine Supplementation Improves Post‐Asphyxial EEG Recovery and Reduces Seizures in Fetal Sheep: Implications for Hypoxic–Ischemic Encephalopathy29
Promise of Nucleic Acid Therapeutics for Amyotrophic Lateral Sclerosis29
Recessive Variants in PIGG Cause a Motor Neuropathy with Variable Conduction Block, Childhood Tremor, and Febrile Seizures: Expanding the Phenotype29
Reply to “Letter on Multiple Acyl‐Coenzyme A Dehydrogenase Deficiency Is Associated with Sertraline Use”29
Histopathological Correlates of Lobar Microbleeds in False‐Positive Cerebral Amyloid Angiopathy Cases28
ANA Podcasts & Webinars: Genetics of Epilepsy28
Pathogenic MAST3 Variants in the STK Domain Are Associated with Epilepsy28
Risk of Multiple Sclerosis in People Living with HIV: An International Cohort Study28
Correction: Decreased Cerebrospinal Fluid Amyloid β 38, 40, 42, and 43 Levels in Sporadic and Hereditary Cerebral Amyloid Angiopathy28
Reply to “Is There an Association between Tuber Involvement of the Fusiform Face Area in Autism Diagnosis?”28
In Memoriam: Arthur Knight Asbury, MD (1928–2022)28
Reply to “VAERS Could Miss or Misinterpret Neurological Side Effects of COVID Vaccinations”28
Issue Information – TOC27
Impact of Time of Day and Season on Outcome in Acute Ischemic Stroke27
Issue Information27
Issue Information27
Search Strategies for Alzheimer Protector Genes27
Subcortical Volumes as Early Predictors of Fatigue in Multiple Sclerosis26
Encephalitis with Autoantibodies against the Glutamate Kainate Receptors GluK226
ANA Investigates: Atrial Fibrillation after Stroke26
Adolescent Headache Due to Congenital Pelvic/Sacral Vascular Malformation26
Pivotal Role of Slitrk1 in Adult Striatal Cholinergic Neurons in Mice: Implication in Tourette Syndrome26
Neuromyelitis Optica Spectrum Disorder: Therapeutic Innovations and Complex Decision‐Making26
Application of the Amyloid/Tau/Neurodegeneration Framework in Cognitively Intact Adults: The CABLE Study26
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Extra Movements in Healthy People: Challenging the Definition and Diagnostic Practice of Tic Disorders26
Evaluation of Soluble Colony Stimulating Factor 1 Receptor (CSF1R) in Peripheral Blood as a Diagnostic Marker of CSF1R‐Related Disorder (CSF1RRD) in a Muri26
Disease‐Modifying Drugs Extend Survival in Hereditary Transthyretin Amyloid Polyneuropathy26
Spoken Language Alterations can Predict Phenoconversion in Isolated Rapid Eye Movement Sleep Behavior Disorder: A Multicenter Study25
CADASIL Affects Multiple Aspects of Cerebral Small Vessel Function on 7T‐MRI25
Cerebral Small Vessel Disease Progression Increases Risk of Incident Parkinsonism25
Emerging Management Challenges Posed by Atrial Fibrillation Detected After Stroke25
Issue Information25
Comparative Safety of Antiseizure Medication Monotherapy for Major Malformations25
α4β2* Nicotinic Cholinergic Receptor Target Engagement in Parkinson Disease Gait–Balance Disorders25
Ultra‐Low Level Somatic Mutations and Structural Variations in Focal Cortical Dysplasia Type II25
“Don't Throw the Baby out with the Bathwater”25
Cinematic Rendering of Extracranial to Intracranial Arterial Bypass25
SRPK3 Is Essential for Cognitive and Ocular Development in Humans and Zebrafish, Explaining X‐Linked Intellectual Disability25
Cortical Correlates of Gait Compensation Strategies in Parkinson Disease25
Smouldering‐Associated Worsening in Multiple Sclerosis: An International Consensus Statement on Definition, Biology, Clinical Implications, and Future Directions25
Annals of Neurology: Volume 95, Number 4, April 202425
Issue Information24
Internal Carotid Artery Pseudoaneurysm and Unilateral Vocal Cord Paralysis Secondary to Parapharyngeal Space Abscess24
Temporal Pattern of Cortical Hypoxia in Multiple Sclerosis and Its Significance on Neuropsychological and Clinical Measures of Disability24
Fixating with the Paretic Eye: Evidence of “Fixation Duress” on PET Imaging24
Brainstem Ischemic Syndrome in NF2‐Related Schwannomatosis24
Annals of Neurology: Volume 96, Number 2, August 202424
NORSE, FIRES, and a Polygenic Trickle of Autoimmunity24
Issue Information24
Issue Information24
Correction to Lyden P, Pryor KE, Coffey CS, et al. Final results of the RHAPSODY trial: a multi‐center, phase 2 trial using a continual reassessment method to determine the safety and toler24
Systemic Metabolic Alteration Dependent on the Thyroid‐Liver Axis in Early PD24
Neutrophils Are Associated with Higher Risk of Incident Amyotrophic Lateral Sclerosis in a BMI‐ and Age‐Dependent Manner23
Prediction of Cognitive Heterogeneity in Parkinson's Disease: A 4‐Year Longitudinal Study Using Clinical, Neuroimaging, Biological and Electrophysiological Biomarkers23
Network Localization of Pediatric Lesion‐Induced Dystonia23
Annual Report from the Editor‐in‐Chief (2024)23
A Carotid Web with Atherosclerotic Plaque23
Intravenous Thrombolysis with Tenecteplase for the Treatment of Acute Ischemic Stroke22
Sex Differences in Trends in Stroke Recurrence and Postrecurrence Mortality 2000–2020: Population‐Based Brain Attack Surveillance in Corpus Christi Project22
Disease Progression in Charcot–Marie–Tooth Disease Related to MPZ Mutations: A Longitudinal Study22
Insular Stimulation Produces Mental Clarity and Bliss22
Diagnosing Epilepsy with Normal Interictal EEG Using Dynamic Network Models22
High Levels of Perivascular Inflammation and Active Demyelinating Lesions at Time of Death Associated with Rapidly Progressive Multiple Sclerosis Disease Course: A Retrospective Postmortem Cohort Stud22
Activated Wake Systems in Narcolepsy Type 122
De Novo Missense Variants in SLC32A1 Cause a Developmental and Epileptic Encephalopathy Due to Impaired GABAergic Neurotransmission22
Salivary CGRP and Erenumab Treatment Response: Towards Precision Medicine in Migraine21
Social Health and Cognitive Change in Old Age: Role of Brain Reserve21
Limbic Stimulation Drives Mania in STN‐DBS in Parkinson Disease: A Prospective Study21
Association of Apolipoprotein E ɛ4 Allele with Enlarged Perivascular Spaces21
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Vessel Wall Imaging of a Carotid Web21
Intrathecal Immunoglobulin M Synthesis is an Independent Biomarker for Higher Disease Activity and Severity in Multiple Sclerosis21
Inflammation in Cerebral Amyloid Angiopathy‐Related Transient Focal Neurological Episodes21
Non–Cell Autonomous Epileptogenesis in Focal Cortical Dysplasia20
Issue Information20
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Reply to “Myelin Oligodendrocyte Glycoprotein Antibody‐Positive Patients Meeting the 2017 McDonald Criteria for Multiple Sclerosis: Challenges in Diagnosis and Treatment Decisions”20
Fostering Academia‐Industry Partnerships to Facilitate Therapeutic Discoveries in Neurology: The Role of ANA as a Catalyst20
Role of the Exposome in Neurodegenerative Disease: Recent Insights and Future Directions20
Annals of Neurology: Volume 92, Number 3, September 202220
MOG‐IgG‐Associated Bilateral Optic Neuritis in Temporal Relation to Monkeypox Vaccination20
Enhancement of Glutamate Uptake as Novel Antiseizure Approach: Preclinical Proof of Concept20
Life‐Limiting Peripheral Organ Dysfunction in Feline Sandhoff Disease Emerges after Effective CNS Gene Therapy20
Hydroxychloroquine for Primary Progressive Multiple Sclerosis20
Charcot Joint20
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Proteomic Indicators of Health Predict Alzheimer's Disease Biomarker Levels and Dementia Risk20
Cognitive Effects of Deep Brain Stimulation in GBA‐Related Parkinson Disease20
Spasticity Predicts Motor Recovery for Patients with Subacute Motor Complete Spinal Cord Injury19
Dominant KPNA3 Mutations Cause Infantile‐Onset Hereditary Spastic Paraplegia19
Re‐Emergence of Poliovirus in the United States: Considerations and Implications19
Cinematic Rendering of Twig‐Like Middle Cerebral Artery19
AI in Neurology: Everything, Everywhere, All at Once Part 3: Surveillance, Synthesis, Simulation, and Systems19
Neuroprotection of Low‐Frequency Repetitive Transcranial Magnetic Stimulation after Ischemic Stroke in Rats19
Phase 1 Evaluation of Elezanumab (Anti–Repulsive Guidance Molecule A Monoclonal Antibody) in Healthy and Multiple Sclerosis Participants19
Postictal Psychosis in Epilepsy: A Clinicogenetic Study19
Networks Underlie Temporal Onset of Dysplasia‐Related Epilepsy: A MELD Study19
Divergent Causes and Convergent Mechanisms of SUDEP18
Longitudinal Alterations of Cerebral Blood Flow in High‐Contact Sports18
MuSK‐Myasthenia Gravis and Cancer18
Microglial and Astrocytic Responses in the Human Midcingulate Cortex in Huntington's Disease18
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Blood‐Based Proteomics for Adult‐Onset Focal Dystonias18
Ablating the Transporter Sodium‐Dependent Dicarboxylate Transporter 3 Prevents Leukodystrophy in Canavan Disease Mice18
Genetically Determined Low‐Density Lipoprotein Cholesterol and Risk of Subarachnoid Hemorrhage18
Pragmatic Clinical Trials in Neurology18
Levodopa Impairs the Energy Metabolism of the Basal Ganglia In Vivo18
Intact HIV Proviruses Persist in the Brain Despite Viral Suppression with ART18
Presynaptic Dopaminergic Imaging Characterizes Patients with REM Sleep Behavior Disorder Due to Synucleinopathy18
Myelin Oligodendrocyte Glycoprotein Antibody‐Positive Patients Meeting the 2017 McDonald Criteria for Multiple Sclerosis: Challenges in Diagnosis and Treatment Decisions18
APOE Antibody Inhibits Aβ‐Associated Tau Seeding and Spreading in a Mouse Model17
Mutations in HID1 Cause Syndromic Infantile Encephalopathy and Hypopituitarism17
Annals of Neurology: Volume 93, Number 4, April 202317
Reply to “Type I IFN Signature in NOTCH1‐Related Leukoencephalopathy”17
Perimesencephalic Hemorrhage from A Superior Cerebellar Artery Dissection17
The Starry Cortex of Aβ‐Related Angiitis17
Cluster Headache Genomewide Association Study and Meta‐Analysis Identifies Eight Loci and Implicates Smoking as Causal Risk Factor17
Annals of Neurology: Volume 90, Number 6, December 202117
Inhibition of Bone Morphogenetic Protein Signaling Prevents Tau Pathology in iPSC Derived Neurons and PS19 Mice17
Thalamic Influence on Slow Wave Slope Renormalization During Sleep17
Annals of Neurology: Volume 95, Number 3, March 202416
Longitudinal Retinal Changes in MOGAD16
Eligibility Rates among Racially and Ethnically Diverse US Participants in Phase 2 and Phase 3 Placebo‐Controlled, Double‐Blind, Randomized Trials of Lecanemab and Elenbecestat in Early Alz16
Association of Mismatch Profiles and Clinical Outcome from Endovascular Therapy in Large Infarct: A Post‐Hoc Analysis of the ANGELASPECT Trial16
Obesity and Multiple Sclerosis Severity: A Mendelian Randomization Study16
Clinically Meaningful Magnetic Resonance Endpoints Sensitive to Preataxic Spinocerebellar Ataxia Types 1 and 316
Cost‐Effectiveness of Endovascular Thrombectomy in Patients with Large Ischemic Stroke16
Characterizing Frontal Lobe Seizure Semiology in Children16
Disparate Dementia Risk Factors Are Associated with Cognitive Impairment and Rates of Decline in African Americans16
Natural History of Leigh Syndrome: A Study of Disease Burden and Progression16
Divergent Associations of Slow‐Wave Sleep versus Rapid Eye Movement Sleep with Plasma Amyloid‐Beta16
Early Treatment with Vigabatrin Does Not Decrease Focal Seizures or Improve Cognition in Tuberous Sclerosis Complex: The PREVeNT Trial16
Characterization of Extracranial Giant Cell Arteritis with Intracranial Involvement and its Rapidly Progressive Subtype16
Amyloid‐Related Imaging Abnormalities in the DIAN‐TU‐001 Trial of Gantenerumab and Solanezumab: Lessons from a Trial in Dominantly Inherited Alzheimer Disease16
Cerebrospinal Fluid Analysis Post–COVID‐19 Is Not Suggestive of Persistent Central Nervous System Infection16
Mutations in CLCN6 as a Novel Genetic Cause of Neuronal Ceroid Lipofuscinosis in Patients and a Murine Model16
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Frequency and Early Predictors of Cognitive Deterioration in Amyotrophic Lateral Sclerosis: A Longitudinal Population‐Based Study15
Annals of Neurology: Volume 96, Number 5, November 202415
In Vivo Assessment of Astrocyte Reactivity in Patients with Progressive Supranuclear Palsy15
Letter on Wine Glass Sign in Bulbar‐Onset Amyotrophic Lateral Sclerosis15
Effect of Mobile Stroke Unit Dispatch in all Patients with Acute Stroke or TIA15
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