Neuropathology and Applied Neurobiology

Article	Citations
Neuronal infection is a major pathogenetic mechanism and cause of fatalities in human acute Nipah virus encephalitis	123
Novel naturally occurring autoantibodies attenuate α‐synuclein pathology in a mouse model of Parkinson's disease	61
An autopsy case of late‐onset spinocerebellar atrophy type 14	51
Oral Abstracts	44
Editorial	32
Potent T cell‐mediated anti‐inflammatory role of the selective CB2 agonist lenabasum in multiple sclerosis	31
Paediatric astroblastoma‐like neuroepithelial tumour of the spinal cord with a MAMLD1‐BEND2 rearrangement	29
Intelligence quotient–genotype association in dystrophinopathies: A systematic review and meta‐analysis	28
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The S1PR2‐CCL2‐BDNF‐TrkB pathway mediates neuroinflammation and motor incoordination in hyperammonaemia	24
Synaptic gene expression changes in frontotemporal dementia due to the MAPT 10 + 16 mutation	23
Anaplastic ganglioglioma—A diagnosis comprising several distinct tumour types	22
A novel SREBF1::NACC1 gene fusion in an unclassifiable intracranial tumour	22
Erratum	21
Rapid bacterial identification from formalin‐fixed paraffin‐embedded neuropathology specimens using 16S rDNA nanopore sequencing	21
Neuronal and astrocytic tetraploidy is increased in drug‐resistant epilepsy	21
Author Index	21
Myostatin in idiopathic inflammatory myopathies: Serum assessment and disease activity	20
Response letter: Complexities in pericyte markers	20
Analysing cerebrospinal fluid with explainable deep learning: From diagnostics to insights	19
Genetic inhibition of PDK1 robustly reduces plaque deposition and ameliorates gliosis in the 5×FAD mouse model of Alzheimer's disease	18
124th Meeting of the British Neuropathological Society The View, Royal College of Surgeons of England, Lincoln's Inn Fields, London	18
Concurrent tau pathologies in frontotemporal lobar degeneration with TDP‐43 pathology	16
A standardised protocol for blood and cerebrospinal fluid collection and processing for biomarker research in ataxia	16

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Cover Image, Volume 50, Issue 3	16
Perineuronal nets are phagocytosed by MMP‐9 expressing microglia and astrocytes in the SOD1G93A ALS mouse model	15
Non‐coding regulatory elements: Potential roles in disease and the case of epilepsy	15
Impaired brain insulin signalling in Parkinson's disease	15
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Issue Information	15
Evidence of neural crest cell origin of a DICER1 mutant CNS sarcoma in a child with DICER1 syndrome and NRAS‐mutant neurocutaneous melanosis	14
Phenotypic and epigenetic heterogeneity in FGFR2‐fused glial and glioneuronal tumours	14
Microglia induce an interferon‐stimulated gene expression profile in glioblastoma and increase glioblastoma resistance to temozolomide	14
Image‐based deep learning reveals the responses of human motor neurons to stress and VCP‐related ALS	14
Adult‐onset Alexander disease with unusual inflammatory features and a novel GFAP mutation in two patients	14
The autophagy‐enhancing drug carbamazepine improves neuropathology and motor impairment in mouse models of Machado–Joseph disease	14
Epigenetic age acceleration is associated with oligodendrocyte proportions in MSA and control brain tissue	14
Fibrodysplasia ossificans progressiva: Histopathological implications of aberrant bone morphogenic protein signalling for CNS dysgenesis	14
Application of Oral Mucosal Epithelial Cells in Noninvasive Pathological Diagnosis of Neuronal Intranuclear Inclusion Disease	14
Robust methylation‐based classification of brain tumours using nanopore sequencing	13
RNA sequencing of peripheral blood in amyotrophic lateral sclerosis reveals distinct molecular subtypes: Considerations for biomarker discovery	13
Low‐grade epilepsy‐associated neuroepithelial tumours with a prominent oligodendroglioma‐like component: The diagnostic challenges	13
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TDP‐43 pathology and functional deficits in wild‐type and ALS/FTD mutant cyclin F mouse models	13
m6A mRNA methylation in human brain is disrupted in Lewy body disorders	13
Hippocampal dentate granule cells in temporal lobe epilepsy: A morphometry and transcriptomic study	12
WNT‐activated, MYC‐amplified medulloblastoma displaying intratumoural heterogeneity	12
The genomic landscape of dysembryoplastic neuroepithelial tumours and a comprehensive analysis of recurrent cases	12
MiR‐142‐3p regulates synaptopathy‐driven disease progression in multiple sclerosis	12
126th Meeting of the British Neuropathological Society The View, Royal College of Surgeons of England, Lincoln's Inn Fields, London	12
Is islet amyloid polypeptide indeed expressed in the human brain?	12
The blood–CSF–brain route of neurological disease: The indirect pathway into the brain	12
Neurotherapeutic implications of sense and respond strategies generated by astrocytes and astrocytic tumours to combat pH mechanical stress	12
Comprehensive analysis of intratumoural heterogeneity of somatic copy number alterations in diffuse glioma reveals clonality‐dependent prognostic patterns	12
Issue Information	11
AKT1E17K‐mutated meningioma cell lines respond to treatment with the AKT inhibitor AZD5363	11
Axonal response of mitochondria to demyelination and complex IV activity within demyelinated axons in experimental models of multiple sclerosis	11
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Intramuscular Nerve Bundles Reflect TDP‐43 Pathology in the Medulla and Spinal Cord of ALS Patients	11
Issue Information	11
Interferon‐gamma contributes to disease progression in the Ndufs4(−/−) model of Leigh syndrome	11
Fibroblast growth factor 9 (FGF9)‐mediated neurodegeneration: Implications for progressive multiple sclerosis?	11
Corrigendum	11
Issue Information	10
Pathological Characterisation of Posterior Cortical Atrophy in Comparison With Amnestic Alzheimer's Disease	10
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Quantitative cellular changes in multiple system atrophy brains	9
Nanopore sequencing identifies Borrelia miyamotoi as an unexpected cause of meningitis after B cell depletion	9
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HnRNP K mislocalisation in neurons of the dentate nucleus is a novel neuropathological feature of neurodegenerative disease and ageing	9
Muscle biopsy practices in the evaluation of neuromuscular disease: A systematic literature review	9
Proteomic profiling of polyglucosan bodies associated with glycogenin‐1 deficiency in skeletal muscle	8
Corrigendum	8

Atypical teratoid/rhabdoid tumour‐TYR subtype arising in the setting of germline ring chromosome 22: An uncommon form of tumour predisposition	8
Low‐grade diffusely infiltrative tumour (LGDIT), SMARCB1‐mutant: A clinical and histopathological distinct entity showing epigenetic similarity with ATRT‐MYC	8
Regional redistribution of CB1 cannabinoid receptors in human foetal brains with Down's syndrome and their functional modifications in Ts65Dn+/+ mice	8
Amino‐terminally elongated Aβ peptides are generated by the secreted metalloprotease ADAMTS4 and deposit in a subset of Alzheimer's disease brains	8
Regulation of CNS pathology by Serpina3n/SERPINA3: The knowns and the puzzles	7
Cytoplasmic HDAC4 recovers synaptic function in the 3×Tg mouse model of Alzheimer's disease	7
Unfolded protein response markers Grp78 and eIF2alpha are upregulated with increasing alpha‐synuclein levels in Lewy body disease	7
Ageing‐related tau astrogliopathy severely affecting the substantia nigra	7
Adult brain tumour research in 2024: Status, challenges and recommendations	7
The SPTLC1 p.S331 mutation bridges sensory neuropathy and motor neuron disease and has implications for treatment	7
Issue Information	7
Letter to the editor	7
GFAP expression in the brain during human postnatal development	7
Diagnostic accuracy of 1p/19q codeletion tests in oligodendroglioma: A comprehensive meta‐analysis based on a Cochrane systematic review	7
A novel homozygous nonsense variant in COL12A1 causes myopathic Ehlers‐Danlos syndrome: A case report and literature review	7
Dysfunction of the blood–brain barrier in Alzheimer's disease: Evidence from human studies	6
Phosphorylation of MAP 1A regulates hyperphosphorylation of Tau in Alzheimer's disease model	6
Mechanisms of COVID‐19‐associated olfactory dysfunction	6
Cerebellar phenotypes in germline PTEN mutation carriers	6
Soluble amyloid‐β dimers are resistant to amyloid‐β prion conversion in vivo suggesting antiprion properties	6
Issue Information	6
125th Meeting of the British Neuropathological Society The View, Royal College of Surgeons of England, Lincoln's Inn Fields, London	6
Issue Information	6
LMNB1‐duplication mediated nuclear architecture alteration and demyelination of cerebral white matter in a patient with ADLD	6
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Psychotic symptoms in frontotemporal dementia with TDP‐43 tend to be associated with type B pathology	6
Cover Image, Volume 50, Issue 1	6
Identification of a novel heterozygous DYSF variant in a large family with a dominantly‐inherited dysferlinopathy	6
Multiplex Immunofluorescent Analysis of Alpha‐Synuclein in Nigral Lewy Bodies With Heat‐Induced Antibody Stripping Reveals an Intricate Multilayered Structure	6
Artificial intelligence in histopathological image analysis of central nervous system tumours: A systematic review	5
Ectopic expression of neuronal adenosine kinase, a biomarker in mesial temporal lobe epilepsy without hippocampal sclerosis	5
PLAG‐Family Amplified CNS Embryonal Tumour With PLAG1 Immunohistochemical Expression: Expanding the Spectrum of Diagnostic Tools	5
Refining Muscle Morphometry Through Machine Learning and Spatial Analysis	5
Methyl donor supplementation reduces phospho‐Tau, Fyn and demethylated protein phosphatase 2A levels and mitigates learning and motor deficits in a mouse model of tauopathy	5
Computational Analysis of SOD1‐G93A Mouse Muscle Biomarkers for Comprehensive Assessment of ALS Progression	5
TAF15 and Transportin 1 in Intranuclear Inclusions of Neuronal Intranuclear Inclusion Disease	5
Analysis of a pituitary tumour with histological features of central neurocytoma points towards the emergence of a new entity recognisable by a specific epigenetic signature	4
Relationships Between Alcohol Intake and Mitochondrial DNA Methylation in the Human Prefrontal Cortex and Nucleus Accumbens	4
Loss of IDH mutation or secondary tumour manifestation? Evolution of an IDH‐mutant and 1p/19q‐codeleted oligodendroglioma after 15 years of continuous temozolomide treatment and radiotherapy: A case r	4
Neuroinvasion via Peripheral Nerves in Epidemic Viral Encephalitis Caused by Enterovirus, Orthoflavivirus and SARS‐Coronavirus	4
Simultaneous Nbs1 and p53 inactivation in neural progenitors triggers high‐grade gliomas	4
Metastatic Bifocal Germinoma With Dramatic Early Steroid Response, Utility of Circulating miR‐371a‐3p and Vinblastine Monotherapy Prior to Definitive Craniospinal Irradiation	4
Standardised TruAI Automated Quantification of Intracellular Neuromelanin Granules in Human Brain Tissue Sections	4
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Long‐standing multiple system atrophy‐Parkinsonism with limbic and FTLD‐type α‐synuclein pathology	4
Classification of diseases with accumulation of Tau protein	4
Issue Information	4
Cortical morphometric vulnerability to generalised epilepsy reflects chromosome‐ and cell type‐specific transcriptomic signatures	4
Distinguishing post‐translational modifications in dominantly inherited frontotemporal dementias: FTLD‐TDP Type A (GRN) vs Type B (C9orf72)	4
The molecular mechanisms that underlie IGHMBP2‐related diseases	4
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Paths to hippocampal damage in neuromyelitis optica spectrum disorders	3
Issue Information	3
Pathological substrate of memory impairment in multiple system atrophy	3
Oxygen treatment reduces neurological deficits and demyelination in two animal models of multiple sclerosis	3
Early loss of locus coeruleus innervation promotes cognitive and neuropathological changes before amyloid plaque deposition in a transgenic rat model of Alzheimer's disease	3
Testing Meningiomas With Methylation Arrays: Insights and Recommendations From a Large Single‐Centre Study	3
A systems‐level analysis highlights microglial activation as a modifying factor in common epilepsies	3
Unveiling the identities of null cell tumours: Epigenomics corroborate subtle histological cues in pituitary neuroendocrine tumour/adenoma classification	3
Skeletal muscle involvement in systemic amyloidosis is often overlooked	3
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Combinatorial model of amyloid β and tau reveals synergy between amyloid deposits and tangle formation	3
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Change in the molecular properties of CH1641 prions after transmission to wild‐type mice: Evidence for a single strain	3
Cover Image, Volume 48, Issue 5	3
Muscleblind‐like 2 knockout shifts adducin 1 isoform expression and alters dendritic spine dynamics of cortical neurons during brain development	3
An Intracerebrally‐Infected Mouse Model of Enterovirus A71 Demonstrates Restricted Inter‐Neuronal Spread Within the Brain Parenchyma Despite Strong SCARB2 Expression	3
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Respiratory chain dysfunction in perifascicular muscle fibres in patients with dermatomyositis is associated with mitochondrial DNA depletion	3
Issue Information	3
Protein Coaggregation in Caribbean Atypical Parkinsonism: The Contribution of Annonacin	2
Diffuse infiltrating tumour with the molecular profile of an atypical teratoid rhabdoid tumour (AT/RT SHH‐1B) in an adult patient	2
The contribution of brain banks to knowledge discovery in amyotrophic lateral sclerosis: A systematic review	2
Post‐mortem 7T MR imaging and neuropathology in middle stage juvenile‐onset Huntington disease: A case report	2
Progressive hemispheric atrophy in HIV: A Rasmussen's‐like variant of CD8 encephalitis?	2
TAPPing into the potential of inducible tau/APP transgenic mice	2
CuII(atsm) significantly decreases microglial reactivity in patients with sporadic amyotrophic lateral sclerosis	2
A high‐throughput single‐cell RNA expression profiling method identifies human pericyte markers	2
Chronic traumatic encephalopathy neuropathologic change in former Australian rugby players	2
Slow disease progression and characteristic TDP‐43 inclusions in a patient with familial amyotrophic lateral sclerosis carrying a TARDBP G357S variant	2

Genotype–Phenotype Correlation in Progressive External Ophthalmoplegia: Insights From a Retrospective Analysis	2
Recurrent posterior fossa group A (PFA) ependymoma in a young child with constitutional mismatch repair deficiency (CMMRD)	2
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Nanoscale reorganisation of synaptic proteins in Alzheimer's disease	2
Pathogenic variants of Valosin‐containing protein induce lysosomal damage and transcriptional activation of autophagy regulators in neuronal cells	2
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Identical Seeding Characteristics and Cryo‐EM Filament Structures in FTLD‐Synuclein and Typical Multiple System Atrophy	2
Tuberous sclerosis complex‐1 (TSC1) contributes to selective neuronal vulnerability in Alzheimer's disease	2
Clinicopathological Characteristics and Immune Microenvironment of Posterior Pituitary Tumours	2
Investigating key factors underlying neurodegeneration linked to alpha‐synuclein spread	2
Elevated expression of urokinase plasminogen activator in rodent models and patients with cerebral amyloid angiopathy	2
A reassessment of spinal cord pathology in severe infantile spinal muscular atrophy	2