Neuropathology and Applied Neurobiology

Article	Citations
Role of Astrocytic and Microglial Phenotype in the Biology of Hippocampal Sclerosis	141
Oral Abstracts	64
Neuronal infection is a major pathogenetic mechanism and cause of fatalities in human acute Nipah virus encephalitis	58
Neuropathological Characterisation of McLeod Syndrome With a Proposed New Grading System	36
Novel naturally occurring autoantibodies attenuate α‐synuclein pathology in a mouse model of Parkinson's disease	33
Editorial	28
Intelligence quotient–genotype association in dystrophinopathies: A systematic review and meta‐analysis	27
An autopsy case of late‐onset spinocerebellar atrophy type 14	25
Paediatric astroblastoma‐like neuroepithelial tumour of the spinal cord with a MAMLD1‐BEND2 rearrangement	25
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Author Index	22
Erratum	22
The S1PR2‐CCL2‐BDNF‐TrkB pathway mediates neuroinflammation and motor incoordination in hyperammonaemia	21
Myopathology and Immune Profile of Granulomatous Myositis in Sarcoid Myopathy	21
Anaplastic ganglioglioma—A diagnosis comprising several distinct tumour types	21
Synaptic gene expression changes in frontotemporal dementia due to the MAPT 10 + 16 mutation	20
Neuronal and astrocytic tetraploidy is increased in drug‐resistant epilepsy	19
Analysing cerebrospinal fluid with explainable deep learning: From diagnostics to insights	18
Response letter: Complexities in pericyte markers	18
A novel SREBF1::NACC1 gene fusion in an unclassifiable intracranial tumour	17
Rapid bacterial identification from formalin‐fixed paraffin‐embedded neuropathology specimens using 16S rDNA nanopore sequencing	17
Perineuronal nets are phagocytosed by MMP‐9 expressing microglia and astrocytes in the SOD1 G93A ALS mouse model	16
Cover Image, Volume 50, Issue 3	16
Myostatin in idiopathic inflammatory myopathies: Serum assessment and disease activity	16

Issue Information	16
124th Meeting of the British Neuropathological Society The View, Royal College of Surgeons of England, Lincoln's Inn Fields, London	16
Genetic inhibition of PDK1 robustly reduces plaque deposition and ameliorates gliosis in the 5×FAD mouse model of Alzheimer's disease	16
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Non‐coding regulatory elements: Potential roles in disease and the case of epilepsy	15
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Concurrent tau pathologies in frontotemporal lobar degeneration with TDP‐43 pathology	15
A standardised protocol for blood and cerebrospinal fluid collection and processing for biomarker research in ataxia	15
Application of Oral Mucosal Epithelial Cells in Noninvasive Pathological Diagnosis of Neuronal Intranuclear Inclusion Disease	15
Adult‐onset Alexander disease with unusual inflammatory features and a novel GFAP mutation in two patients	14
Epigenetic age acceleration is associated with oligodendrocyte proportions in MSA and control brain tissue	14
TDP‐43 pathology and functional deficits in wild‐type and ALS/FTD mutant cyclin F mouse models	14
Phenotypic and epigenetic heterogeneity in FGFR2 ‐fused glial and glioneuronal tumours	14
Fibrodysplasia ossificans progressiva: Histopathological implications of aberrant bone morphogenic protein signalling for CNS dysgenesis	14
m6A mRNA methylation in human brain is disrupted in Lewy body disorders	14
Evidence of neural crest cell origin of a DICER1 mutant CNS sarcoma in a child with DICER1 syndrome and NRAS‐mutant neurocutaneous melanosis	14
RNA sequencing of peripheral blood in amyotrophic lateral sclerosis reveals distinct molecular subtypes: Considerations for biomarker discovery	13
Microglia induce an interferon‐stimulated gene expression profile in glioblastoma and increase glioblastoma resistance to temozolomide	13
Robust methylation‐based classification of brain tumours using nanopore sequencing	13
The genomic landscape of dysembryoplastic neuroepithelial tumours and a comprehensive analysis of recurrent cases	13
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126th Meeting of the British Neuropathological Society The View, Royal College of Surgeons of England, Lincoln's Inn Fields, London	13
Intramuscular Nerve Bundles Reflect TDP‐43 Pathology in the Medulla and Spinal Cord of ALS Patients	12
The blood–CSF–brain route of neurological disease: The indirect pathway into the brain	12
Comprehensive analysis of intratumoural heterogeneity of somatic copy number alterations in diffuse glioma reveals clonality‐dependent prognostic patterns	12
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Fibroblast growth factor 9 (FGF9)‐mediated neurodegeneration: Implications for progressive multiple sclerosis?	12
Neurotherapeutic implications of sense and respond strategies generated by astrocytes and astrocytic tumours to combat pH mechanical stress	12
Hippocampal dentate granule cells in temporal lobe epilepsy: A morphometry and transcriptomic study	12
Interferon‐gamma contributes to disease progression in the Ndufs4 (−/−) model of Leigh syndrome	12
Issue Information	12
WNT‐activated, MYC ‐amplified medulloblastoma displaying intratumoural heterogeneity	12
Is islet amyloid polypeptide indeed expressed in the human brain?	12
Axonal response of mitochondria to demyelination and complex IV activity within demyelinated axons in experimental models of multiple sclerosis	11
Issue Information	11
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Issue Information	10
Nanopore sequencing identifies Borrelia miyamotoi as an unexpected cause of meningitis after B cell depletion	10
Corrigendum	10
Muscle biopsy practices in the evaluation of neuromuscular disease: A systematic literature review	10
Low‐grade diffusely infiltrative tumour (LGDIT), SMARCB1‐mutant: A clinical and histopathological distinct entity showing epigenetic similarity with ATRT‐MYC	9
Quantitative cellular changes in multiple system atrophy brains	9
AKT1 E17K ‐mutated meningioma cell lines respond to treatment with the AKT inhibitor AZD5363	9
Atypical teratoid/rhabdoid tumour‐TYR subtype arising in the setting of germline ring chromosome 22: An uncommon form of tumour predisposition	9
HnRNP K mislocalisation in neurons of the dentate nucleus is a novel neuropathological feature of neurodegenerative disease and ageing	9
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Amino‐terminally elongated Aβ peptides are generated by the secreted metalloprotease ADAMTS4 and deposit in a subset of Alzheimer's disease brains	9
Corrigendum	9
Pathological Characterisation of Posterior Cortical Atrophy in Comparison With Amnestic Alzheimer's Disease	9
The SPTLC1 p.S331 mutation bridges sensory neuropathy and motor neuron disease and has implications for treatment	8

Diagnostic accuracy of 1p/19q codeletion tests in oligodendroglioma: A comprehensive meta‐analysis based on a Cochrane systematic review	8
Adult brain tumour research in 2024: Status, challenges and recommendations	8
Proteomic profiling of polyglucosan bodies associated with glycogenin‐1 deficiency in skeletal muscle	8
Cytoplasmic HDAC4 recovers synaptic function in the 3×Tg mouse model of Alzheimer's disease	8
Regulation of CNS pathology by Serpina3n/SERPINA3: The knowns and the puzzles	8
GFAP expression in the brain during human postnatal development	7
Letter to the editor	7
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Unfolded protein response markers Grp78 and eIF2alpha are upregulated with increasing alpha‐synuclein levels in Lewy body disease	7
Ageing‐related tau astrogliopathy severely affecting the substantia nigra	7
A novel homozygous nonsense variant in COL12A1 causes myopathic Ehlers‐Danlos syndrome: A case report and literature review	7
Cerebellar phenotypes in germline PTEN mutation carriers	7
Regional redistribution of CB1 cannabinoid receptors in human foetal brains with Down's syndrome and their functional modifications in Ts65Dn +/+ mic	7
Mechanisms of COVID‐19‐associated olfactory dysfunction	7
Cover Image, Volume 50, Issue 1	6
Identification of a novel heterozygous DYSF variant in a large family with a dominantly‐inherited dysferlinopathy	6
Multiplex Immunofluorescent Analysis of Alpha‐Synuclein in Nigral Lewy Bodies With Heat‐Induced Antibody Stripping Reveals an Intricate Multilayered Structure	6
125th Meeting of the British Neuropathological Society The View, Royal College of Surgeons of England, Lincoln's Inn Fields, London	6
LMNB1 ‐duplication mediated nuclear architecture alteration and demyelination of cerebral white matter in a patient with ADLD	6
Issue Information	6
Dysfunction of the blood–brain barrier in Alzheimer's disease: Evidence from human studies	6
Soluble amyloid‐β dimers are resistant to amyloid‐β prion conversion in vivo suggesting antiprion properties	6
Issue Information	6
Issue Information	5
Metastatic Bifocal Germinoma With Dramatic Early Steroid Response, Utility of Circulating miR‐371a‐3p and Vinblastine Monotherapy Prior to Definitive Craniospinal Irradiation	5
Relationships Between Alcohol Intake and Mitochondrial DNA Methylation in the Human Prefrontal Cortex and Nucleus Accumbens	5
Refining Muscle Morphometry Through Machine Learning and Spatial Analysis	5
TAF15 and Transportin 1 in Intranuclear Inclusions of Neuronal Intranuclear Inclusion Disease	5
Ectopic expression of neuronal adenosine kinase, a biomarker in mesial temporal lobe epilepsy without hippocampal sclerosis	5
Computational Analysis of SOD1‐G93A Mouse Muscle Biomarkers for Comprehensive Assessment of ALS Progression	5
Psychotic symptoms in frontotemporal dementia with TDP‐43 tend to be associated with type B pathology	5
Methyl donor supplementation reduces phospho‐Tau, Fyn and demethylated protein phosphatase 2A levels and mitigates learning and motor deficits in a mouse model of tauopathy	5
Issue Information	5
PLAG‐Family Amplified CNS Embryonal Tumour With PLAG1 Immunohistochemical Expression: Expanding the Spectrum of Diagnostic Tools	5
Artificial intelligence in histopathological image analysis of central nervous system tumours: A systematic review	5
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Analysis of a pituitary tumour with histological features of central neurocytoma points towards the emergence of a new entity recognisable by a specific epigenetic signature	4
Loss of IDH mutation or secondary tumour manifestation? Evolution of an IDH‐mutant and 1p/19q‐codeleted oligodendroglioma after 15 years of continuous temozolomide treatment and radiotherapy: A case r	4
Phosphorylation of MAP 1A regulates hyperphosphorylation of Tau in Alzheimer's disease model	4
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An Intracerebrally‐Infected Mouse Model of Enterovirus A71 Demonstrates Restricted Inter‐Neuronal Spread Within the Brain Parenchyma Despite Strong SCARB2 Expression	4
Long‐standing multiple system atrophy‐Parkinsonism with limbic and FTLD‐type α‐synuclein pathology	4
Cover Image, Volume 48, Issue 5	4
Distinguishing post‐translational modifications in dominantly inherited frontotemporal dementias: FTLD‐TDP Type A ( GRN ) vs Type B (	4
Standardised TruAI Automated Quantification of Intracellular Neuromelanin Granules in Human Brain Tissue Sections	4
Classification of diseases with accumulation of Tau protein	4
Muscleblind‐like 2 knockout shifts adducin 1 isoform expression and alters dendritic spine dynamics of cortical neurons during brain development	4
Skeletal muscle involvement in systemic amyloidosis is often overlooked	4
The molecular mechanisms that underlie IGHMBP2 ‐related diseases	4
Pathological substrate of memory impairment in multiple system atrophy	4
Cortical morphometric vulnerability to generalised epilepsy reflects chromosome‐ and cell type‐specific transcriptomic signatures	4
Correction to “Neuropathological Characterisation of McLeod Syndrome With a Proposed New Grading System”	4
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Simultaneous Nbs1 and p53 inactivation in neural progenitors triggers high‐grade gliomas	4
Issue Information	4
Neuroinvasion via Peripheral Nerves in Epidemic Viral Encephalitis Caused by Enterovirus, Orthoflavivirus and SARS‐Coronavirus	4
Early loss of locus coeruleus innervation promotes cognitive and neuropathological changes before amyloid plaque deposition in a transgenic rat model of Alzheimer's disease	3
Change in the molecular properties of CH1641 prions after transmission to wild‐type mice: Evidence for a single strain	3
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Cu II (atsm) significantly decreases microglial reactivity in patients with sporadic amyotrophic lateral sclerosis	3
Pathogenic variants of Valosin‐containing protein induce lysosomal damage and transcriptional activation of autophagy regulators in neuronal cells	3
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Testing Meningiomas With Methylation Arrays: Insights and Recommendations From a Large Single‐Centre Study	3
Paths to hippocampal damage in neuromyelitis optica spectrum disorders	3
Nanoscale reorganisation of synaptic proteins in Alzheimer's disease	3
Protein Coaggregation in Caribbean Atypical Parkinsonism: The Contribution of Annonacin	3
A reassessment of spinal cord pathology in severe infantile spinal muscular atrophy	3
Oxygen treatment reduces neurological deficits and demyelination in two animal models of multiple sclerosis	3
Respiratory chain dysfunction in perifascicular muscle fibres in patients with dermatomyositis is associated with mitochondrial DNA depletion	3
Combinatorial model of amyloid β and tau reveals synergy between amyloid deposits and tangle formation	3
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Chronic traumatic encephalopathy neuropathologic change in former Australian rugby players	3
Diffuse infiltrating tumour with the molecular profile of an atypical teratoid rhabdoid tumour (AT/RT SHH‐1B) in an adult patient	3
Issue Information	3
Unveiling the identities of null cell tumours: Epigenomics corroborate subtle histological cues in pituitary neuroendocrine tumour/adenoma classification	3
TAPPing into the potential of inducible tau/APP transgenic mice	2
The contribution of brain banks to knowledge discovery in amyotrophic lateral sclerosis: A systematic review	2
A high‐throughput single‐cell RNA expression profiling method identifies human pericyte markers	2
Clinicopathological Characteristics and Immune Microenvironment of Posterior Pituitary Tumours	2

Recurrent posterior fossa group A (PFA) ependymoma in a young child with constitutional mismatch repair deficiency (CMMRD)	2
Identical Seeding Characteristics and Cryo‐EM Filament Structures in FTLD‐Synuclein and Typical Multiple System Atrophy	2
DNA methylation‐based classification of glioneuronal tumours synergises with histology and radiology to refine accurate molecular stratification	2
Investigating key factors underlying neurodegeneration linked to alpha‐synuclein spread	2
Elevated expression of urokinase plasminogen activator in rodent models and patients with cerebral amyloid angiopathy	2
Slow disease progression and characteristic TDP‐43 inclusions in a patient with familial amyotrophic lateral sclerosis carrying a TARDBP G357S variant	2
Issue Information	2
Post‐mortem 7T MR imaging and neuropathology in middle stage juvenile‐onset Huntington disease: A case report	2
Three‐Dimensional Visualisation of Blood Vessels in Human Gliomas Using Tissue Clearing and Deep Learning	2
Novel Aspects of Hereditary Spastic Paraplegia: A Clinicopathologic and Biochemical Study of a Patient With a Heterozygous GCH1 Variant	2
A Variant of OTUD3 in Early‐Onset Parkinsonism	2
Genotype–Phenotype Correlation in Progressive External Ophthalmoplegia: Insights From a Retrospective Analysis	2
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Tuberous sclerosis complex‐1 (TSC1) contributes to selective neuronal vulnerability in Alzheimer's disease	2
Progressive hemispheric atrophy in HIV: A Rasmussen's‐like variant of CD8 encephalitis?	2
DNA methylation profiling improves routine diagnosis of paediatric central nervous system tumours: A prospective population‐based study	2