Muscle & Nerve

Article	Citations
	110
A clinical bulbar assessment scale (CBAS) for amyotrophic lateral sclerosis	95
Join AANEM	68
AANEM News and Insights	62
The neuromuscular fellowship portal and match	60
An atypical case of pure motor neuropathy with proximal limb weakness and polyphasic course	59
AANEM Calender of Events	58
Issue Information	55
AANEM News & Insights	52
Longitudinal Outcomes Among Patients With Duchenne Muscular Dystrophy: A Canadian Retrospective Population‐Based Study	47
Longitudinal specialty palliative care for people with amyotrophic lateral sclerosis using a universal referral method	41
Skeletal muscle symptoms and quantitative MRI in females with dystrophinopathy	40
Diagnostic yield of advanced genetic testing in patients with hereditary neuropathies: A retrospective single‐site study	37
Pilot study of a virtual weight management program for Duchenne muscular dystrophy	35
Concentric Needle Jitter Measurements in Voluntarily Activated Deltoid Muscle in Healthy Control Subjects	32
Cardiopulmonary exercise testing on adaptive equipment in children and adults with Friedreich ataxia	32
Electrodiagnostic reporting preferences of referring physicians: An exploratory survey	32
A 5‐year natural history cohort of patients with facioscapulohumeral muscular dystrophy determining disease progression and feasibility of clinical outcome assessments for clinical trials	31
Facial nerve vulnerability in spinal muscular atrophy and motor unit number index of the orbicularis oculi muscle	31
Diagnosis of Primary Mitochondrial Diseases	28
Paraneoplastic Anti‐Contactin‐1 Autoimmune Nodopathy	28
Identifying amyotrophic lateral sclerosis through interactions with an internet search engine	27
Combination of stem cells and nerve guide conduit for the treatment of peripheral nerve injury: A meta‐analysis	26
Diagnosis and management of metabolic myopathies	25
Neuromuscular ultrasound: Impact on diagnosis and management	25

Amyotrophic lateral sclerosis represents corticomotoneuronal system failure	25
The impact of genotype on outcomes in individuals with Duchenne muscular dystrophy: A systematic review	25
Are Women Physicians Underrecognized for National Awards in Neuromuscular and Electrodiagnostic Medicine? An Observational Study	24
Axial muscle involvement in patients with limb girdle muscular dystrophy type R9	24
Neuroma morphology: A macroscopic classification system	24
Diagnosis and treatment of hereditary transthyretin amyloidosis with polyneuropathy in the United States: Recommendations from a panel of experts	23
Estimation of diaphragm depth based on waist circumference in the Thai population	22
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Nerve ultrasound characteristics of immunoglobulin M neuropathy associated with anti‐myelin‐associated glycoprotein antibodies	21
Volumetric muscle composition analysis in sporadic inclusion body myositis using fat‐referenced magnetic resonance imaging: Disease pattern, repeatability, and natural progression	20
A case of neuroleukemiosis: The usefulness of nerve ultrasound as a diagnostic tool	19
Issue Information	19
The strength of associations between ultrasound measures of upper limb muscle morphology and isometric muscle strength: An exploratory study	19
AANEM News and Comments	18
Optimal timing of needle electromyography to diagnose lesion severity in traumatic radial nerve injury	18
AANEM Application	18
Optimal placement for needle electromyography of the supinator muscle: Cadaveric studies	18
Value and pitfalls of imaging and electrodiagnosis in neurogenic thoracic outlet syndrome: Lessons learned from present and past	18
Reliability of confocal corneal microscopy for measurement of dendritic cell density in suspected small fiber neuropathy	17
Atypical presentation of hypokalemic periodic paralysis: A case report	17
Redundant nerve roots on magnetic resonance imaging can predict ongoing denervation in patients with lumbar spinal stenosis	17
Pregnancy outcomes in patients with congenital myasthenic syndromes	17
Initiation of noninvasive ventilation in patients with amyotrophic lateral sclerosis	16
Diagnostic criteria in amyotrophic lateral sclerosis: Time for a change	16
Quantitative muscle echointensity: A practical approach using ultrasound to evaluate children with suspected neuromuscular disorders	16
Amyotrophic lateral sclerosis mimics	16
Impact of COVID‐19 on the quality of life of patients with neuromuscular disorders in the Lombardy area, Italy	15
Rasch analysis of the Unidimensional Self‐Efficacy Scale in Neuromuscular Disorders and comparison between sex, age, and diagnoses	15
Peripheral nerve injuries in the performing artist	15
Psychometric evaluation of modified spinal muscular atrophy functional rating scale (SMAFRS) in adult patients using Rasch analysis	15
Onasemnogene abeparvovec gene therapy for spinal muscular atrophy: A cohort study from the United Arab Emirates	15
Join AANEM	15
Issue Highlights	15
Positive acetylcholine receptor antibody in nonmyasthenic patients	15
The utility of diaphragm ultrasound thickening indices for assessing respiratory decompensation in amyotrophic lateral sclerosis	15
Pembrolizumab‐induced radiation recall myopathy with fasciopathy: A case report	15
AANEM News and Insights	15
Bilateral hemidiaphragm atrophy and electrical myotonia in anti‐muscle specific tyrosine kinase myasthenia gravis	15
Intermittent versus daily regimen of prednisolone in ambulatory boys with Duchenne muscular dystrophy: A randomized, open‐label trial	15
Low T3 syndrome is associated with peripheral neuropathy in patients with type 2 diabetes mellitus	14
Myotonia congenita in a Greek cohort: Genotype spectrum and impact of the CLCN1:c.501C > G variant as a genetic modifier	14
Identifying Daytime Hypercapnia Using Transcutaneous Carbon Dioxide Monitoring in Patients With Amyotrophic Lateral Sclerosis	14
Sustained clinical benefit following systemic gene replacement therapy in Duchenne muscular dystrophy	14
	13
Utilization of MG‐ADL in myasthenia gravis clinical research and care	13
Issue Highlights	13
Elevation of fast but not slow troponin I in the circulation of patients with Becker and Duchenne muscular dystrophy	13
The supraclavicular nerve	13
Autophagy in non–immune‐mediated rhabdomyolysis: Assessment of p62 immunohistochemistry	13
Epidemiology of seropositive myasthenia gravis in Sardinia: A population‐based study in the district of Sassari	12

Issue Highlights	12
Understanding the role of the lower motor neuron in spinal cord injury and its impact on electrodiagnostic assessment	12
Acquired hyperexcitable peripheral nerve disorders: Clinical and laboratory features, therapeutic responses, and long‐term follow‐up	12
A‐waves are associated with neuropathic pain in leprosy	12
Clinical profile and impact of comorbidities in patients with very‐late‐onset myasthenia gravis	11
Cardiac and pulmonary findings in dysferlinopathy: A 3‐year, longitudinal study	11
AANEM News and Insights	11
Fatigue and Fatigability in Spinal Muscular Atrophy; a Proposed Taxonomy to Enhance Assessment and Treatment	11
Effects of cardiac medications on ventricular function in patients with Duchenne muscular dystrophy–related cardiomyopathy	11
Segmental motor neuron dysfunction in amyotrophic lateral sclerosis: Insights from H reflex paradigms	11
Adult‐onset nemaline myopathy due to a novel homozygous variant in the TNNT1 gene	11
Pain in acute motor axonal neuropathy	11
Issue Highlights	11
Intravenous immunoglobulin and plasma exchange prescribing patterns for Guillain‐Barre Syndrome in the United States—2001 to 2018	11
Utility of Carpal Tunnel Release and Ulnar Decompression in CMT1A and HNPP	11
Guidelines for ethical behavior relating to clinical practice issues in neuromuscular and electrodiagnostic medicine	11
Implications of median sensory study to the thumb and deltoid/biceps motor unit recruitment on identifying C6 root avulsion in upper neonatal brachial plexus palsy	11
Exercise as Medicine in Neuromuscular Disorders: Changing Attitudes, Ongoing Challenges, and Future Research Directions	11
Issue Highlights	11
Ultrasound‐guided transforaminal approach for nusinersen delivery in adult spinal muscle atrophy patients with challenging access	11
Autologous hematopoietic stem cell transplant for the treatment of refractory myasthenia gravis with anti‐muscle specific kinase antibodies	11
Factors associated with increased health‐related quality‐of‐life benefits in hereditary transthyretin amyloidosis polyneuropathy patients treated with inotersen	11
Extraocular muscle volume on time‐of‐flight magnetic resonance angiography in patients with myasthenia gravis	10
Evaluation of mechanomyogram efficacy as a tool for assessing paired‐pulse inhibition of blink reflex early R1 component	10
AANEM 2024 Annual Meeting Abstracts Guide	10
Bone Health Determinants in Ambulant Prepubertal Boys With Duchenne Muscular Dystrophy Treated With Deflazacort: Findings From a 3‐Year Study	10
Assessing perspectives of disease burden and clinically meaningful changes using the Spinal Muscular Atrophy Health Index in adolescents and young adults	10
Effects of hypobaric hypoxia during a simulated ultra‐long‐haul flight on inflammation and regeneration after muscle trauma and muscle trauma‐hemorrhagic shock	10
Voluntary and magnetically evoked muscle contraction protocol in males with Duchenne muscular dystrophy: Safety, feasibility, reliability, and validity	10
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Prevalence of Pathogenic Transthyretin Gene Variants in the Rocky Mountain Region	10
Prevalence of cardiovascular implantable electronic devices in children with type 1 myotonic dystrophy	10
Serial electrodiagnostic studies in acute partial conduction block from cyclist's palsy	10
Calendar of Events	10
Associations between lower extremity muscle fat fraction and motor performance in myotonic dystrophy type 2: A pilot study	10
Evaluation of the applicability of weak shoulder and arm sparing signs in amyotrophic lateral sclerosis by multiple neurologists and neurology residents: A single‐center study	10
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Measuring treatment response to chronic inflammatory demyelinating polyneuropathy in clinical practice: More than just asking	9
Standardization of Myasthenia Gravis Outcome Measures in Clinical Practice: A Report of the MGFA Task Force	9
Radial motor nerve conduction studies recorded from triceps brachii and extensor carpi radialis longus: Techniques and reference values	9
Issue Information	9
Issue Information	9
Reply to “Intravenous saline may not be a placebo in patients with small fiber neuropathy”	9
A phase Ib/IIa, open‐label, multiple ascending‐dose trial of domagrozumab in fukutin‐related protein limb‐girdle muscular dystrophy	9
AANEM News and Comments	9
Assessment of clinical factors affecting outcome of myasthenia gravis	9
Paraproteinemic neuropathies	9
Milestones of progression in myotonic dystrophy type 1 and type 2	9
MScanFit motor unit number estimation of human anconeus muscle	8
Join AANEM	8
Mass effect of the distal triceps brachii muscle on ulnar nerve movement during elbow flexion	8
Calendar of Events	8
Pregnancy planning may impact maternal and neonatal outcomes in people with myasthenia gravis	8
Changes in electrophysiological findings suggestive of demyelination following Guillain‐Barré syndrome: A retrospective study	8
Incidence and causes of overdiagnosis of myasthenia gravis	8
Details Matter: The Difference Between NIV and NVS	8
Issue Information	8
Racial Disparities in ALS Progression: Time to Clinical Events Observed in a Single Center	8
Ten years of riluzole use in a tertiary ALS clinic	8
Effectiveness and Safety of IVIG for the Treatment of HMGCR Immune‐Mediated Necrotizing Myopathy	8
Laryngospasm in amyotrophic lateral sclerosis	8
Issue Highlights	8
Could posturography be a useful outcome measure for chronic inflammatory demyelinating polyneuropathy?	8
Neuromuscular Ultrasound Training: Bridging the Gap	8
The Enigma of the Motor Nerve Conduction Study	8
Assessment of clinical skills in electrodiagnostic medicine	8
Short‐term educational value of online neuromuscular ultrasound courses	8
Infiltrative arteriovenous malformation of the sciatic nerve: Imaging and management	8
Ultrasonic evidence of mononeuritis multiplex caused by Lyme neuroborreliosis	8
Single center experience with hourglass‐like constriction neuropathy of suprascapular nerve	8
The effect of methocarbamol and mexiletine on murine muscle spindle function	7
Correction to “Myositis‐Related Autoantibody Profile and Clinical Characteristics Stratified by Anti‐Cytosolic 5′‐Nucleotidase 1A Status in Connective Tissue Diseases”	7
GNE myopathy: Don't sleep on the platelets	7
Electrodiagnostic and ultrasound evaluation of respiratory weakness	7
Electrophysiology to identify disease mechanisms in CIDP: Reliability and value	7
Join AANEM	7
Thymoma Associated Myasthenia Gravis Successfully Treated With Ravulizumab	7
Perceived exertion is not a substitute for fatiguability in spinal muscular atrophy	7
Phantom radiculopathy: An electrodiagnostic challenge	7
Age‐related sensory neuropathy in patients with spinal muscular atrophy type 1	7

AANEM Application	7
The CAPN3 p.Lys 254del variant is not always associated with dominant CAPN3‐related muscular dystrophy	7
AANEM News and Comments	7
Hyperhomocysteinemia in patients with riboflavin‐responsive multiple acyl‐CoA dehydrogenase deficiency	7
Evaluating longitudinal therapy effects via the North Star Ambulatory Assessment	7
High prevalence of paraspinal muscle involvement in adults with McArdle disease	7
The use and misuse of sonographic reference values in neuromuscular disease	7
Utility of Median Nerve Electrophysiological Parameters in Differentiating Immune‐Mediated Demyelination From Compressive Median Neuropathy at the Wrist	7
The quality of occupational healthcare for carpal tunnel syndrome, healthcare expenditures, and disability outcomes: A prospective observational study	7
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Three‐dimensional quantitative muscle ultrasound in patients with facioscapulohumeral dystrophy and myotonic dystrophy	7
Issue Highlights	7
A novel homozygous ALPK3 variant associated with cardiomyopathy and skeletal muscle involvement	7
Composite nerve conduction scores and signs for diagnosis and somatic staging of diabetic polyneuropathy: Mid North American ethnic cohort survey	7
Chronic ataxic neuropathy, ophthalmoplegia, immunoglobulin M paraprotein, cold agglutinins, and disialosyl antibodies presenting after COVID19 mRNA vaccination	7
Updated consensus statement: Intravenous immunoglobulin in the treatment of neuromuscular disorders report of the AANEM ad hoc committee	6
Lung volume recruitment improves volitional airway clearance in amyotrophic lateral sclerosis	6
Statin‐associated anti–3‐hydroxy‐3‐methyl‐glutaryl‐coenzyme A reductase (HMGCR) myopathy: Imaging findings on thigh‐muscle magnetic resonance imaging (MRI) in six patients	6
Nerve Ultrasound Detects Nerve Atrophy in Patients With Ataxia‐Telangiectasia: A Pilot Study	6
Quantifying adverse events: The burden is on us!	6
The diagnosis of myasthenia gravis: The sensitive issue of specificity	6
	6
AANEM Calender of Events	6
A cross‐sectional study of memory and executive functions in patients with sporadic inclusion body myositis	6
Burden of illness and costs in patients with myasthenia gravis currently receiving treatment in the United States	6
Prognostic factors, disease course, and treatment efficacy in Duchenne muscular dystrophy: A systematic review and meta‐analysis	6
Home‐based gait analysis as an exploratory endpoint during a multicenter phase 1 trial in limb girdle muscular dystrophy type R2 and facioscapulohumeral muscular dystrophy	6
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“An Ounce of Prevention…”	6
Issue Information	6
Myofibrillar myopathy presenting with an inclusion bodymyositis‐likephenotype	6
Brachial multisegmental muscle weakness and atrophy caused by a spinal CSF leak after lumbo‐peritoneal shunting	6
Exploring caregivers' attitudes and beliefs about nutrition and weight management for young people with Duchenne muscular dystrophy	6
Long‐term safety and functional outcomes of delandistrogene moxeparvovec gene therapy in patients with Duchenne muscular dystrophy: A phase 1/2a nonrandomized trial	6
Serious Neurologic Adverse Events in Tofersen Clinical Trials for Amyotrophic Lateral Sclerosis	6
Myasthenia gravis Lambert–Eaton overlap syndrome: Recommended modification for the diagnostic criteria	6
Myotonic dystrophy type 1: A comparison between the adult‐ and late‐onset subtype	6
Cardiopulmonary exercise performance and factors associated with aerobic capacity in neuromuscular diseases	6
Relationship Between Quantitative Magnetic Resonance Imaging Measures and Functional Changes in Patients With Duchenne Muscular Dystrophy	6
Combining multiple measures into a summary index: A step toward more reliable measurement	6
Join AANEM	6
ALS patient and caregiver attitudes toward physician‐hastened death in California	6
The difference in nerve ultrasound and motor nerve conduction studies between autoimmune nodopathy and chronic inflammatory demyelinating polyneuropathy	6
Factors influencing the decision to introduce alternative nutrition in patients with Duchenne muscular dystrophy	5
Issue Information	5
Neuromuscular Ultrasound Training in Neuromuscular Fellowship Programs in Canada: Minding the Gap	5
The best and worst of times in therapy development for myasthenia gravis	5
Feasibility of intrathecal therapeutic injections in spinal muscular atrophy patients via a percutaneous transsacral hiatus route: An initial neuroimaging morphometric study	5
Ted M. Burns MD	5
Recurrent motor branch neuropathy in carpal tunnel syndrome: An ultrasound study	5
AANEM News and Insights	5
Respiratory considerations in patients with neuromuscular disorders	5
Proceedings of the 22nd Annual Meeting of the Northeast ALS Consortium	5
COVID‐19 infection in patients with late‐onset Pompe disease	5
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Issue Information	5
Eculizumab in refractory generalized myasthenia gravis previously treated with rituximab: subgroup analysis of REGAIN and its extension study	5
Electrical impedance myography in healthy volunteers	5
Calendar of Events	5
Time course of capillary regression and an expression balance between vascular endothelial growthfactor‐Aand thrombospondin‐1 in the soleus muscle of hindlimb unloaded rats	5
AANEM News & Insights	5
Pathological features of reinnervated skeletal muscles after crush injury of the sciatic nerve in ob/ob mice	5
In Memorium: Jun Kimura, MD	5
Small Fiber Neuropathy and SARS‐CoV‐2 Infection. Another piece in the long COVID puzzle?	5
Late‐onset Becker muscular dystrophy with distal muscle weakness and rimmed vacuoles	5
Refining quality measures for electrodiagnostic testing in suspected carpal tunnel syndrome to account for acceptable variations in practice: Expert review process	5
Alterations in fast‐twitch muscle membrane conductance regulation do not explain decreased muscle function of SOD1G93A rats	5
Differences in corneal nerve fiber density and fiber length in patients with painful chronic idiopathic axonal polyneuropathy and diabetic polyneuropathy	5
AANEM Application	5
Gene transfer therapy in children with spinal muscular atrophy: A single‐center experience with a cohort of 25 children	5
Which combined nerve conduction study scores are best suited for polyneuropathy in diabetic patients?	5
Slowing the loss of physical function in amyotrophic lateral sclerosis with edaravone: Post hoc analysis of ALSFRS‐R item scores in pivotal study MCI186‐19	5
Cubital tunnel perfusion in different postures—An anatomical investigation	5
Does specificity of electrodiagnostic test referrals predict test outcome in children?	5
No sex‐based differences in odds of starting or time to treatment of generalized myasthenia gravis: A single center cohort study	5
Usefulness and prognostic value of diagnostic tests in patients with possible chronic inflammatory demyelinating polyradiculoneuropathy	5
Hyperexcitability of the asymptomatic motor cortex in a case of Mills' syndrome	5
AANEM News & Insights	5
The impact of myasthenia gravis severity on work and daily activities	5
Issue Information	5
Dominant and recessive congenital myasthenic syndromes caused by SYT2 mutations	5
COVID‐19–accelerated disease progression in two patients with amyotrophic lateral sclerosis	5
AANEM News and Insights	5
Sarcolemmal Excitability Properties of the Trapezius	5
The use of electrical stimulation to enhance recovery following peripheral nerve injury	5
Transcutaneous carbon dioxide monitoring in ALS: Assessment of hypoventilation heats up	5
Nasal cannulas for pediatric neuromuscular respiratory home management—Perhaps a too well‐kept secret?	5
Periodic paralysis due to cumulative effects of rare variants in SCN4A with small functional alterations	4
Issue Highlights	4
Oculopharyngodistal myopathy: The recent discovery of an old disease	4
Issue Information	4
Calendar of Events	4
Ultrasound‐guided motor unit scanning electromyography	4
Longitudinal relationships between free‐living activities, fatigue, and symptom severity in myasthenia gravis using cohort and individualized models	4
Ultrasonographic evaluation of ulnar nerve morphology in patients with ulnar nerve instability	4